Nrhiav
Kaw lub thawv tshawb nrhiav no.

Muaj txiaj ntsig txuas rau koj

Lwm yam Lymphoma

Nyem qhov no mus saib lwm hom lymphoma

Thawj Qhov Ntsab Nruab Nrab Nruab Nrab Txheej Nruab Nrab Lymphoma (PCNSL)

Primary central nervous system lymphoma, abbreviated as PCNSL, yog ib qho tsis tshua muaj, aggressive (ceev-loj hlob) sub-hom non-Hodgkin lymphoma (NHL), uas tsim nyob rau hauv lub hlwb thiab / los yog txha caj qaum. Nws feem ntau tshwm sim rau cov neeg muaj hnub nyoog 50 thiab 60s tab sis tuaj yeem tshwm sim rau txhua lub hnub nyoog.

Nws muaj ntau dua rau PCNSL nyob hauv koj lub hlwb, tab sis nws tuaj yeem nyob hauv txhua qhov chaw ntawm koj CNS. Nyob ib ncig ntawm 1 ntawm 50 lub hlwb hlav yog ib hom CNS lymphoma.

Lub lumbar puncture tuaj yeem siv los kuaj xyuas cov qog ntshav qog ntshav hauv koj lub paj hlwb hauv nruab nrab, lossis xa cov tshuaj khomob rau hauv koj lub hlwb txha caj qaum.

Lymphoma yog ib hom qog nqaij hlav ntawm cov qe ntshav dawb hu ua lymphocytes thiab tuaj yeem faib ua hom Hodgkin, lossis Non-Hodgkin Lymphoma. Primary central nervous system lymphoma (PCNSL) yog ib yam uas tsis tshua muaj, aggressive hom Non-Hodgkin Lymphoma pom nyob rau hauv koj lub hauv nruab nrab paj hlwb (CNS) uas muaj xws li koj lub hlwb, qaum qaum thiab ob lub qhov muag. Cov qog nqaij hlav qog nqaij hlav hauv PCNSL hu ua B-cell lymphocytes.

Nplooj ntawv no yuav muab cov ntaub ntawv koj xav tau rau koj yog tias tab tom ntsib cov tsos mob thiab cov tsos mob, hauv kev kuaj mob, pib kho PCNSL, lossis muaj cov kev mob tshwm sim uas cuam tshuam nrog kev kho mob rau PCNSL.

Ntawm nplooj ntawv no:

Primary central nervous system lymphoma (PCNSL) fact sheet PDF

Txheej txheem cej luam ntawm PCNSL

PCNSL txhim kho thaum mob qog noj ntshav B-cell lymphocytes (B-cells) tsim nyob rau hauv cov ntaub so ntswg lymphoid ntawm lub hlwb thiab / lossis qaum qaum. PCNSL kuj tseem tuaj yeem pib hauv cov khaubncaws sab nraud povtseg ntawm lub hlwb (meninges) lossis hauv qhov muag (ocular lymphoma). 

Qee zaum lymphoma tuaj yeem pib hauv lwm qhov chaw ntawm lub cev thiab kis mus rau CNS. Qhov no yog defferent rau PCNSL thiab raug kho txawv ib yam nkaus. Yog tias nws tau pib sab nraud ntawm CNS thiab kis mus rau CNS nws hu ua Secondary CNS lymphoma.

Qhov ua rau PCNSL tsis paub zoo li yog kis ntawm ntau lymphomas. Cov neeg muaj feem cuam tshuam rau hnub nyoog ntawm 50 txog 60 xyoo, nrog rau qhov nruab nrab hnub nyoog ntawm kev kuaj mob nyob ib ncig ntawm 60 xyoo, txawm li cas los xij nws tuaj yeem tshwm sim rau txhua lub hnub nyoog. PCNSL kuj tseem tshwm sim me ntsis hauv cov neeg uas muaj lub cev tsis muaj zog, uas yuav tshwm sim los ntawm:

  • HIV (human immunodeficiency virus) kab mob - qhov no tsis tshua muaj tshwm sim tam sim no vim muaj cov tshuaj tiv thaiv kab mob zoo.
  • Cov tshuaj - cov uas siv los tiv thaiv lub cev tiv thaiv kab mob, xws li tom qab hloov lub cev lossis lwm hom kev tiv thaiv kab mob rau cov kab mob autoimmune xws li mob caj dab rheumatoid.

Puas yog PCNSL kho tau?

Ntau tus lymphomas nruj heev tuaj yeem teb tau zoo rau kev kho mob nrog kws khomob vim tias kev siv tshuaj khomob ua haujlwm los ntawm kev tua cov cell loj hlob sai. Muaj ntau ntau yam, txawm li cas los xij, qhov cuam tshuam seb koj puas yuav kho tau los ntawm koj tus mob lymphoma lossis tsis. Ntau tus neeg tuaj yeem kho tau, lwm tus yuav muaj lub sijhawm tshem tawm - qhov twg tsis muaj cov tsos mob ntawm lymphoma nyob hauv koj lub cev, tab sis tom qab ntawd nws tuaj yeem rov qab los (rov qab los) thiab xav tau kev kho mob ntxiv.

Yog xav paub ntxiv txog koj txoj hauv kev yuav kho tau, tham nrog koj tus kws kho mob hematologist lossis oncologist.

Central Nervous System (CNS) ua dab tsi?

cov cov leeg hauv nruab nrab (CNS) yog ib feem ntawm peb lub cev uas tswj tag nrho peb lub cev ua haujlwm. Nws suav nrog peb lub hlwb, qaum qaum thiab ob lub qhov muag.

Lub hlwb

Peb lub hlwb yog tsim los ntawm:

  • Lub paj hlwb - qhov no tswj peb cov lus thiab kev nkag siab, peb cov kev xav thiab kev yeem txav mus los (cov kev txav peb txiav txim siab ua)
  • cerebellum - pab nrog txav thiab tswj peb qhov sib npaug
  • Lub Hlwb - tswj cov haujlwm tseem ceeb hauv lub cev, xws li peb ua pa, lub plawv dhia thiab ntshav siab

Tus txha nqaj qaum

Peb tus txha caj qaum khiav los ntawm peb lub hlwb mus rau peb sab nraub qaum hauv cov pob txha ntawm tus txha nraub qaum. Ib cov hlab ntsha txuas ncaj qha mus rau tus txha caj qaum. Cov hlab ntsha nqa cov ntaub ntawv hais txog kev hnov ​​​​qab ntawm lub cev thiab nqa cov lus mus rau thiab los ntawm peb lub hlwb mus rau tag nrho peb lub cev, tswj peb cov leeg, thiab tag nrho peb lub cev ua haujlwm.

Peb CNS tiv thaiv li cas?

Peb CNS raug cais tawm ntawm peb lub cev thiab tiv thaiv kev raug mob, kis kab mob thiab kab mob ntau txoj hauv kev.

  • cov meninges yog cov txheej txheem tiv thaiv ntawm cov ntaub so ntswg uas npog lub paj hlwb thiab txha caj qaum - qhov no yog qhov ua rau mob 'meningitis'
  • Cov kua dej tshwj xeeb hu ua 'cerebrospinal kua'(CSF) nyob ib puag ncig lub hlwb thiab txha caj qaum kom cushion lawv - nws muaj nyob rau hauv qhov chaw nruab nrab ntawm meninges thiab lub hlwb thiab qaum qaum.
  • cov ntshav-hlwb barrier nyob ib puag ncig peb lub hlwb - nws yog qhov thaiv ntawm cov hlwb thiab cov hlab ntsha uas tsuas yog cia qee yam khoom nkag mus rau lub hlwb. Qhov no tiv thaiv nws los ntawm cov tshuaj phem thiab kab mob, thiab nws tseem tiv thaiv lossis cuam tshuam nrog ntau cov tshuaj khomob uas dhau los ntawm cov ntshav mus rau lub hlwb.
Txhawm rau nkag siab txog PCNSL koj yuav tsum paub me ntsis txog koj li B-Cell lymphocytes.

B-Cell lymphocytes:

  • Yog hom ntshav dawb
  • Tiv thaiv kab mob thiab kab mob kom koj noj qab haus huv. 
  • Nco ntsoov cov kab mob uas koj tau muaj yav dhau los, yog li yog tias koj kis tau tus kab mob zoo ib yam ntxiv, koj lub cev tiv thaiv kab mob tuaj yeem tua nws tau zoo dua thiab sai. 
  • Ua nyob rau hauv koj cov pob txha pob txha (qhov spongy nyob rau hauv nruab nrab ntawm koj cov pob txha), tab sis feem ntau nyob rau hauv koj lub lymphatic system uas muaj xws li koj: 
  1. cov mob ua paug
  2. lymphatic hlab ntsha thiab lymph kua
  3. lub cev - spleen, thymus, tonsils, appendix
  4. lymphoid cov ntaub so ntswg
  • Muaj peev xwm taug kev los ntawm koj lub cev lymphatic, mus rau txhua qhov ntawm koj lub cev los tiv thaiv kab mob lossis kab mob. 
Koj lub cev lymphatic yog ib feem ntawm koj lub cev tiv thaiv kab mob thiab ua rau koj noj qab haus huv los ntawm kev sib ntaus cov kab mob. Nws suav nrog koj cov qog nqaij hlav, cov hlab ntsha lymphatic thiab cov kabmob xws li koj tus po, thymus thiab lwm yam. Koj B-cell lymphocytes feem ntau nyob hauv koj lub cev lymphatic.
Yuav ua li cas thaum PCNSL txhim kho?

PCNSL txhim kho thaum muaj qog nqaij hlav qog nqaij hlav hauv koj lub hauv nruab nrab lub paj hlwb (CNS), uas suav nrog koj lub hlwb, qaum qaum, ob lub qhov muag, cov hlab ntsha cranial thiab cov txheej txheem tiv thaiv ntawm cov ntaub so ntswg uas npog koj lub hlwb thiab txha caj qaum hu ua meninges.

Thaum koj muaj PCNSL, koj cov qog nqaij hlav qog noj ntshav:

  • Loj hlob uncontrollably
  • Yuav tsis ua haujlwm zoo los tiv thaiv kab mob thiab kab mob
  • Nws tuaj yeem loj dua li qhov lawv yuav tsum tau thiab tuaj yeem saib txawv rau koj cov B-hlwb noj qab haus huv 
  • Yuav ua rau lymphoma tsim nyob rau hauv koj lub hlwb, qaum qaum thiab ob lub qhov muag.
  • Vim tias muaj kev tiv thaiv ib puag ncig peb CNS, PCNSL feem ntau tsis kis mus rau lwm qhov ntawm koj lub cev zoo li lwm hom qog ntshav qog ntshav, txawm li cas los xij, qee zaum lawv tuaj yeem kis cov qog ntshav hauv cov txiv neej.

Cov tsos mob thaum lymphoma nyob hauv koj qhov Central Nervous System (CNS)

Cov tsos mob ntawm lymphoma hauv koj CNS muaj feem xyuam rau kev ua haujlwm ntawm koj lub hlwb, qhov muag thiab qaum qaum. Lawv yuav nyob ntawm seb qhov twg ntawm koj CNS cuam tshuam thiab yuav suav nrog cov hauv qab no:

  • mob taub hau
  • hloov rau koj lub zeem muag
  • tsis meej pem los yog kev nco hloov
  • kev hloov hauv kev nco qab (ua tsaug zog thiab tsis teb)
  • nyuaj hais lus lossis nqos
  • hloov ntawm koj lub siab xav lossis tus cwj pwm
  • qaug dab peg (fits)
  • xeev siab thiab ntuav
  • poob qab los noj mov (tsis xav noj) thiab poob phaus
  • nyuaj mus rau chav dej
  • nyuaj taug kev, tsis khov los yog ntog
  • qaug zog, loog los yog tingling kev xav.

Kev kuaj mob, theem thiab muab qhab nia ntawm PCNSL

Yog tias koj tus kws kho mob xav tias koj yuav muaj lymphoma koj yuav tsum tau kuaj ntau yam. Tsis zoo li lwm hom kab mob qog nqaij hlav, kev ua haujlwm tsis ua tiav yog tias koj muaj PCNSL vim tias cov qog ntshav qog ntshav nyob hauv koj lub hauv nruab nrab lub paj hlwb (CNS). Ib qho kev sib kis sab nraud ntawm CNS feem ntau tsuas yog nyob rau hauv cov txiv neej thiab tsuas yog rau cov noob qes xwb. 

PCNSL ib txwm suav hais tias yog qib qog ntshav qog ntshav siab txhais tau hais tias nws hnyav heev. Nws loj hlob sai thiab tuaj yeem txav los ntawm koj CNS sai. Cov qog nqaij hlav B-hlwb (lymphoma cells) kuj zoo li txawv ntawm koj cov B-hlwb noj qab haus huv vim lawv loj hlob sai heev thiab tsis muaj sijhawm los tsim kom zoo.

Nyem rau ntawm nqe lus hauv qab no kom paub ntau ntxiv txog hom kev xeem uas koj yuav tau kuaj xyuas, thiab kawm ntxiv txog koj tus PCNSL.

Qhov nqaij me

Txhawm rau kuaj xyuas PCNSL koj yuav xav tau kev kuaj ntshav. Biopsy yog ib txoj kev tshem tawm ib feem, lossis tag nrho cov qog nqaij hlav los yog cov ntaub so ntswg cuam tshuam. Thaum lub sij hawm tus txheej txheem koj yuav muaj ib tug general los yog hauv zos tshuaj loog ua kom koj xis nyob, los yog kom paub tseeb tias koj tsis tsaug zog thaum nws ua tiav.

Hom biopsy yuav tsum tau ua yuav nyob ntawm seb qhov lymphoma nyob qhov twg.

Yog tias lymphoma xav tias nyob hauv koj:

  • Lub paj hlwb - tus kws kho mob hlwb (tus kws kho mob tshwj xeeb hauv kev kuaj mob thiab kho cov teeb meem nrog CNS) siv lub hlwb biopsy. Cov pob (lossis cov qauv ntawm cov pob txha) hauv koj lub hlwb yuav raug muab tshem tawm siv CT scan los pab coj cov koob txhaj tshuaj mus rau qhov chaw zoo. Qhov no hu ua a 'stereotactic biopsy'. Koj yuav muaj tshuaj loog dav dav rau cov txheej txheem no vim nws tseem ceeb tsis txhob txav mus los.
  • Qhov muag - tus kws kho qhov muag (tus kws kho mob tshwj xeeb hauv cov kab mob thiab kev raug mob ntawm lub qhov muag) yuav siv me ntsis ntawm cov vitreous (gel zoo li cov khoom hauv koj lub qhov muag) txhawm rau kuaj cov qog ntshav qog ntshav.
  • Kab laug sab - tus kws kho hluav taws xob tshwj xeeb tuaj yeem kuaj xyuas koj tus txha nraub qaum.

Kev kuaj ntshav

Kev kuaj ntshav kuj tseem raug coj los kuaj xyuas koj cov qog ntshav qog ntshav, tab sis kuj tseem nyob hauv kev kho mob kom tus kws kho mob tuaj yeem nkag siab zoo txog koj txoj kev noj qab haus huv tag nrho, thiab xyuas kom koj lub cev ua haujlwm tau zoo los tiv thaiv kev kho mob.

Qhov kev tshuaj ntsuam no feem ntau muab cov duab zoo tshaj plaws ntawm koj lub hlwb thiab lwm qhov chaw ntawm CNS thiab tuaj yeem kuaj xyuas tus txha caj qaum.

MRI
MRI scan ntawm lub hlwb

Cov kev kuaj no feem ntau yog ua kom pom cov qog ntshav qog ntshav nyob rau lwm qhov hauv lub cev. Lawv muab cov duab ntxaws uas muab cov ntaub ntawv ntau dua li tus qauv X-ray. Tej zaum lawv kuj yuav ua tau los saib cov pob txha ntawm koj tus txha nraub qaum.

CT scan

Hom kev tshuaj ntsuam no feem ntau siv ua ke nrog CT scan txhawm rau txheeb xyuas cov qog ntshav qog ntshav nyob rau lwm qhov hauv koj lub cev. Nws yuav siv ib daim duab ntawm sab hauv ntawm koj lub cev tag nrho. Koj yuav tau txais ib koob nrog qee cov tshuaj uas muaj cov qog nqaij hlav cancer xws li lymphoma hlwb, nqus. Cov tshuaj pab PET scan kom paub seb qhov lymphoma nyob qhov twg thiab qhov loj thiab cov duab los ntawm kev qhia txog thaj chaw nrog cov qog ntshav qog ntshav. Tej zaum cov no yog hu ua "kub".  

Raws li PCNSL tuaj yeem cuam tshuam rau lub qhov muag koj kuj yuav xav tau ntau yam kev kuaj mob ophthalmic. Tus kws kho qhov muag (tus kws kho qhov muag tshwj xeeb) yuav siv lub ophthalmoscope - ib qho cuab yeej nrog lub teeb thiab lub lens me me - kom pom qhov zoo hauv koj lub qhov muag. Qee qhov kev kuaj pom yuav ua tiav thiab cov no pab tus kws kho qhov muag saib cov qog thiab saib seb puas muaj mob qog noj ntshav.

 

Tej zaum yuav xav tau ib qho biopsy ntawm qhov muag. Qhov no hu ua vitrectomy. Ib qho cuab yeej me me tau muab tso rau hauv lub qhov muag thiab nws yuav siv cov qauv ntawm jelly-zoo li vitreous, uas yog cov khoom uas ua rau nruab nrab ntawm lub qhov muag.

Testicular ultrasound rau cov txiv neej yog ib qho kev kuaj uas tau txais cov duab ntawm cov noob qes thiab cov ntaub so ntswg nyob ib ncig ntawm lub scrotum. Qhov ultrasound no yuav ua tau raws li qee qhov PCNSL tuaj yeem kis mus rau cov qog.

tau

Tos rau tag nrho koj cov txiaj ntsig tuaj yeem yog lub sijhawm ntxhov siab rau koj thiab koj cov neeg koj hlub. Nws yog ib qho tseem ceeb los tham txog qhov koj xav li cas thiab qhib siab nrog cov neeg nyob ib puag ncig koj txog yam koj xav tau. Ntau tus neeg xav pab, tab sis tsis paub yuav ua li cas los ntawm kev qhia rau lawv paub tias koj xav tau dab tsi, koj tuaj yeem pab lawv muab kev txhawb nqa koj xav tau.

Nws kuj tseem yuav pab tau pib npaj qhov koj xav tau hauv lub hlis tom ntej yog tias koj xav tau kev kho mob. Peb tau muab qee cov lus qhia ua ke ntawm Peb Lub Neej Nrog Lymphoma - Cov Khoom Siv Hauv Lub Vev Xaib. Nyem rau ntawm qhov txuas hauv qab no kom coj mus rau nplooj ntawv ntawd.

Koj tseem tuaj yeem tiv tauj peb Tus Kws Kho Mob Xov Xwm Kub Ceev kom tham nrog ib tus kws kho mob Lymphoma. Tsuas yog nyem rau ntawm Hu rau peb khawm nyob hauv qab ntawm nplooj ntawv no.

Koj kuj tseem nyiam koom nrog ib qho ntawm peb nplooj ntawv social media los tham nrog lwm tus neeg nyob nrog. Txuas nrog peb cov nplooj ntawv social media los ntawm txhaj cov kev sib txuas rau saum toj ntawm nplooj ntawv.

Rau ntau info saib
Nyob nrog Lymphoma - Cov Khoom Siv Tau

Kev kho mob rau PCNSL

Muaj cov ntaub ntawv raug cai tuaj yeem pab koj muaj kev ntseeg siab thiab paub tias yuav xav li cas, thiab tuaj yeem pab koj npaj ua ntej rau yam koj xav tau. Tab sis nws tuaj yeem nyuaj kom paub cov lus nug dab tsi thaum koj tab tom pib kho. Yog koj tsis paub, koj tsis paub dab tsi, koj yuav paub li cas nug?

Peb tau muab tso ua ke ib daim ntawv teev cov lus nug uas koj yuav pom muaj txiaj ntsig. Tau kawg, txhua tus neeg qhov xwm txheej yog qhov tshwj xeeb, yog li cov lus nug no tsis npog txhua yam, tab sis lawv pib zoo. Nyem rau ntawm qhov txuas hauv qab no kom pom cov ntawv PDF uas koj tuaj yeem rub tawm thiab luam tawm yog tias koj nyiam.

Nyem qhov no mus download tau Cov Lus Nug los nug koj tus kws kho mob ua ntej pib kho.

Fertility preservation

Txawm hais tias koj yog txiv neej lossis poj niam, ntau yam kev kho mob qog noj ntshav tuaj yeem cuam tshuam rau koj txoj kev xeeb tub - koj lub peev xwm ua rau menyuam mos. Yog tias koj xav kom muaj menyuam tom qab kev kho mob, lossis tsis paub tseeb tias koj xav tau, nrog koj tus kws kho mob tham txog cov kev xaiv uas muaj los pab tiv thaiv koj txoj kev xeeb tub thaum kho.

Txheej txheem cej luam ntawm hom kev kho mob

Nyem rau ntawm cov slides hauv qab no kom pom cov ntsiab lus ntawm ntau hom kev kho mob uas koj tuaj yeem muab los kho koj tus PCNSL.

Kev kho mob steroid
Koj yuav zoo li yuav pib ntawm steroids thaum koj tau ua tiav koj qhov biopsies. Steroids pab txo qhov o nyob ib ncig ntawm qhov chaw ntawm lymphoma thiab tuaj yeem pab txhim kho koj cov tsos mob. Lawv feem ntau yog pib tom qab biopsies vim tias lymphoma tuaj yeem mob hnyav dua yog tias cov tshuaj steroids twb tau muab lawm.

Txawm li cas los xij, yog tias koj muaj cov tsos mob hnyav thiab koj tus kws kho mob muaj kev ntseeg siab tias koj muaj PCNSL, lawv tuaj yeem xaiv pib cov tshuaj steroids txhawm rau txhim kho koj cov tsos mob txawm tias ua ntej koj kuaj ntshav.

Steroids kuj yog tshuaj lom rau cov qog ntshav qog ntshav kom lawv tuaj yeem pab txo qis cov qog ntshav qog ntshav thaum tos lwm yam kev kho mob pib.

Cov tshuaj steroids tuaj yeem muab tso rau hauv cov hlab ntsha (los ntawm txoj hlab ntsha) lossis qhov ncauj (los ntawm qhov ncauj). Ib qho tshuaj steroid yog dexamethasone.
Kev kho mob (chemotherapy)
Tej zaum koj yuav muaj cov tshuaj no ua ib ntsiav tshuaj thiab/los yog muab tso rau hauv koj cov hlab ntsha (hauv koj cov hlab ntsha) ntawm lub tsev kho mob cancer lossis tsev kho mob. Chemo tua cov cell loj hlob sai yog li nws muaj txiaj ntsig zoo tiv thaiv cov qog ntshav qog ntshav, tab sis kuj tuaj yeem cuam tshuam qee yam ntawm koj lub hlwb zoo uas loj hlob sai, ua rau tsis muaj kev phiv.

Cov kws khomob uas koj tau txais rau PCNSL yuav txawv rau cov neeg uas muaj lwm hom qog ntshav qog ntshav, vim tias cov tshuaj yuav tsum hla koj cov ntshav-hlwb thaiv kom nkag mus rau koj cov lymphoma. Nws yog ib qho uas yuav tsum tau siv tshuaj khomob nrog kev tiv thaiv kab mob xws li rituximab.
Monoclonal antibody
Monoclonal antibodies qee zaum hu ua immunotherapy vim tias lawv pab koj lub cev tiv thaiv kab mob kom paub thiab tua cov qog ntshav qog ntshav.

Tej zaum koj yuav muaj MAB infusion ntawm lub tsev kho mob cancer lossis tsev kho mob. MABs txuas rau lymphoma cell thiab nyiam lwm yam kab mob-tawm cov qe ntshav dawb thiab cov proteins rau cov qog nqaij hlav kom koj lub cev tiv thaiv kab mob tuaj yeem tiv thaiv PCNSL.
Kev Kho Mob Tuav Hluav Taws Xob
Radiotherapy siv hluav taws xob tua cov qog nqaij hlav cancer. Nws zoo li lub zog X-rays thiab ua haujlwm txhua hnub, feem ntau txij hnub Monday txog Friday rau ob peb lub lis piam.

Kev kho mob hlwb tag nrho feem ntau yog siv los ua kev kho mob sib koom ua ke tom qab siv tshuaj khomob.

Txog thaum nruab nrab-nineties nws yog qhov kev kho mob tseem ceeb rau PCNSL, tab sis tam sim no nws tau muab nrog kev kho mob. Consolidation kev kho mob tsom kom txo tau qhov kev pheej hmoo ntawm relapse (lub lymphoma rov qab). Kev kho hluav taws xob tuaj yeem siv los ntawm nws tus kheej yog tias koj tsis tuaj yeem zam cov tshuaj khomob.
Qia cell hloov
Yog tias koj tseem hluas thiab muaj cov qog ntshav qog ntshav siab, SCT yuav raug pom zoo ua kev kho mob, txawm hais tias qhov kev kho no tsis haum rau txhua tus.

SCT ua tiav los hloov koj cov pob txha mob nrog cov kab mob tshiab uas tuaj yeem loj hlob mus rau cov qe ntshav tshiab. Nrog rau SCT, cov qia hlwb raug tshem tawm ntawm cov ntshav. Cov qia hlwb tuaj yeem raug tshem tawm los ntawm tus neeg pub dawb lossis sau los ntawm koj tom qab koj tau txais tshuaj khomob.

Yog tias cov qia hlwb los ntawm tus neeg pub dawb, nws yog hu ua kev hloov pauv ntawm cov qia hlwb. Yog tias koj tus kheej qia hlwb raug sau, nws yog hu ua autologous stem cell transplant.
Previous swb
Tom ntej no swb

Kev kho thawj kab

Koj yuav tau pib kho sai sai tom qab tag nrho koj cov txiaj ntsig tau rov qab los. Qee zaum, tej zaum koj yuav pib ua ntej tag nrho cov txiaj ntsig kev xeem yuav nyob hauv. Nws tuaj yeem nyuaj heev thaum koj pib kho. Tej zaum koj yuav muaj ntau yam kev xav txog seb koj yuav tiv thaiv li cas, tswj xyuas hauv tsev li cas, lossis koj yuav mob npaum li cas.

Qhia rau koj pab neeg kho mob paub yog tias koj xav tias koj yuav xav tau kev pab ntxiv. Tej zaum lawv yuav tuaj yeem pab tau los ntawm kev xa koj mus ntsib tus neeg ua haujlwm hauv zej zog lossis lwm tus kws saib xyuas kev noj qab haus huv los pab koj ua haujlwm tawm qee qhov kev nyuaj hauv kev ua neej txhua hnub uas koj yuav ntsib. Koj tseem tuaj yeem ncav cuag tus Kws Saib Xyuas Mob Lymphoma los ntawm nyem rau ntawm "Tshem rau peb" khawm nyob hauv qab ntawm nplooj ntawv no.

Thaum koj pib kho thawj zaug, nws yog hu ua 'kev kho thawj kab'. Tej zaum koj yuav muaj ntau dua ib yam tshuaj, thiab cov no yuav suav nrog kev kho hluav taws xob, tshuaj khomob lossis tshuaj tiv thaiv kab mob monoclonal.

Tus qauv thawj kab kev kho mob tuaj yeem suav nrog:

 Cov koob tshuaj methotrexate 

Qhov no tuaj yeem ua ke nrog lossis tsis muaj cov tshuaj tiv thaiv monoclonal, rituximab.

 MATRix

Qhov no yog kev sib xyaw ntawm cov tshuaj khomob sib txawv thiab cov tshuaj tiv thaiv monoclonal - methotrexate, cytarabine, thiotepa thiab rituximab - rau PCNSL tshiab.

R-MPV (Pib XNUMX thiab Ntu XNUMX)

Ib feem - Monoclonal antibody (rituximab) thiab kev sib xyaw ntawm cov tshuaj khomob suav nrog methotrexate, procarbazine thiab vincristine.

Qhov thib ob - Tshuaj kho mob siab - cytarabine

Methotrexate thiab cytarabine

Kev sib xyaw ua ke ntawm ob txoj kev kho mob rau PCNSL tshiab.

Intrathecal kws khomob

Qhov no yog chemotherapy uas tau muab rau hauv cov kua dej txha caj qaum los ntawm kev siv lub lumbar puncture. Qhov no ua tiav yog tias pom muaj lymphoma hauv koj tus txha caj qaum.

Kev koom tes nrog kev sim tshuaj

Cov no yuav suav nrog kev sim tshuaj rau kev kho mob thiab lwm yam kev kho mob. Nug koj tus kws kho mob seb koj puas tsim nyog tau txais kev kho mob thawj zaug.

Radiotherapy lossis Stem Cell Transplant

Yog hais tias tus lymphoma teb rau chemotherapy, koj pab neeg kho mob tej zaum yuav qhia tag nrho cov hlwb radiotherapy los yog ib tug autologous qia cell hloov (saib saum toj). Cov no yog cov kev kho mob sib sau ua ke, uas txhais tau hais tias lawv tau siv los txo qhov kev pheej hmoo ntawm kev rov qab los tom qab kev kho mob zoo.

Ob kab thiab kev kho mob tsis tu ncua

Yog tias koj CNS lymphoma relapses (rov qab los) los yog refractory (tsis teb) rau kev kho mob, tej zaum yuav muaj lwm yam kev kho mob.

Kev kho mob uas koj muaj yog tias koj rov qab los lossis muaj cov tshuaj tiv thaiv PCNSL yog hu ua kev kho mob thib ob. Kev kho mob nyob ntawm seb koj haum npaum li cas thaum lub sijhawm, kev kho koj twb tau muaj lawm thiab seb cov lymphoma cuam tshuam rau koj li cas. Koj tus kws kho mob tuaj yeem tham nrog koj los ntawm koj cov kev xaiv, uas yuav suav nrog:

  • Kev siv tshuaj kho mob hnyav dua (muaj zog dua), tej zaum ua raws li kev hloov pauv ntawm cov qia cell (tsis haum rau qee tus neeg).
  • Radiotherapy - yog tias nws tseem tsis tau muab.
  • Palliative kho mob muab nrog lub hom phiaj los txo cov tsos mob.
  • Kev koom tes nrog kev sim tshuaj.

soj ntsuam hlw kom qis

Nws raug pom zoo tias txhua lub sijhawm koj yuav tsum pib kho tshiab koj nug koj tus kws kho mob txog kev sim tshuaj koj yuav tsim nyog tau txais.

Kev sim tshuaj kho mob yog ib txoj hauv kev tseem ceeb los nrhiav cov tshuaj tshiab, lossis kev sib xyaw ntawm cov tshuaj los txhim kho kev kho mob PCNSL yav tom ntej. Lawv kuj tuaj yeem muab sijhawm rau koj sim tshuaj tshiab, ua ke ntawm cov tshuaj lossis lwm yam kev kho mob uas koj yuav tsis tuaj yeem tawm sab nraud ntawm qhov kev sim. Yog tias koj txaus siab koom nrog hauv kev sim tshuaj, nug koj tus kws kho mob seb qhov kev sim tshuaj twg koj tsim nyog tau txais. 

Muaj ntau yam kev kho mob thiab kev kho mob tshiab ua ke uas tam sim no raug sim hauv kev sim tshuaj thoob ntiaj teb rau cov neeg uas tau kuaj pom tshiab thiab rov ua dua tshiab / refractory PCNSL. Qee qhov kev kho mob hauv kev tshawb nrhiav yog:

  • Ibrutinib (Imbruvica®)
  • Zanubrutinib (Brukinsa®) thiab Tiselizumab
  • Pembrolizumab (Keytruda®)
  • GB5121 - Lub hlwb nkag tau BTK inhibitor
Rau ntau info saib
Kev mob tshwm sim ntawm kev kho mob

Nkag siab txog kev sim tshuaj

Kev kuaj mob rau PCNSL

Prognosis yog lo lus siv los piav qhia txog txoj hauv kev uas yuav ua rau koj tus kab mob, nws yuav teb li cas rau kev kho mob thiab koj yuav ua li cas thaum thiab tom qab kho.

Muaj ntau ntau yam uas ua rau koj qhov kev mob tshwm sim thiab nws tsis tuaj yeem muab cov lus qhia tag nrho txog kev kwv yees.

Cov xwm txheej uas tuaj yeem cuam tshuam txog kev kwv yees

 Qee yam uas yuav cuam tshuam koj qhov kev mob tshwm sim muaj xws li:

  • Koj lub hnub nyoog thiab kev noj qab haus huv tag nrho thaum lub sijhawm kuaj mob
  • Koj teb li cas rau kev kho mob

Qee zaum cov tsos mob ntawm CNS lymphoma daws sai sai nrog kev kho mob. Kev kho mob pib nrog steroids tuaj yeem ua tau zoo heev hauv kev txo cov tsos mob. Txawm li cas los xij, cov paj hlwb loj hlob qeeb heev, thiab qee zaum nws tuaj yeem siv sijhawm ntev rau cov tsos mob kom zoo. Qee tus ntawm koj tuaj yeem pom kev txhim kho ntawm cov tsos mob, qee qhov txawm li cas los xij, yuav pom cov tsos mob yuav tsis daws tau tag nrho, tshwj xeeb tshaj yog tias lawv nyob ua ntej kho.

Tau txais kev pab txhawb

Koj pab neeg kho mob tuaj yeem pab txhawb koj txoj kev rov zoo los ntawm kev xa koj mus rau cov kws kho mob uas tsim nyog. Yog tias koj muaj cov leeg tsis muaj zog thiab tsis muaj zog lossis tsis rov qab los sai, koj yuav tsum xav txog kev mus ntsib tus kws kho mob lub cev thiab / lossis tus kws kho mob ua haujlwm vim lawv tuaj yeem muab kev pab thiab tswv yim los txhim kho lub neej zoo. Lawv cov kev pab kuj tseem tuaj yeem tso tseg cov tsos mob tsis zoo los yog lwm yam teeb meem tshwm sim nyob rau lub sijhawm ntev.

Psychologists tuaj yeem muab kev txhawb nqa yog tias muaj teeb meem kev txawj ntse (xav), xws li teeb meem nco lossis saib xyuas. Cov kws kho mob hlwb thiab cov kws pab tswv yim tuaj yeem txhawb nqa nrog kev xav ntawm koj cov qog ntshav qog ntshav.

Nws yog ib qho tseem ceeb uas yuav tsum nco ntsoov tias cov tswv yim kho mob rau PCNSL tau txhim kho zoo heev nyob rau xyoo tas los no. Txawm li cas los xij, PCNSL tuaj yeem kho tau nyuaj, thiab qee qhov kev kho mob muaj kev pheej hmoo ua rau muaj teeb meem rau lub paj hlwb mus ntev (teeb meem ntawm lub hlwb thiab qhov muag). Cov teeb meem no yuav tshwm sim ntau dua yog tias koj raug kuaj mob CNS lymphoma thaum koj laus dua.  

 

Survivorship - Nyob nrog, thiab tom qab mob qog noj ntshav

Txoj kev ua neej noj qab nyob zoo, lossis qee qhov kev hloov pauv ntawm txoj kev ua neej zoo tom qab kev kho mob tuaj yeem pab tau zoo rau koj txoj kev rov zoo. Muaj ntau yam uas koj tuaj yeem ua tau los pab koj nyob zoo tom qab Burkitt. 

Ntau tus neeg pom tias tom qab kuaj mob qog noj ntshav, lossis kev kho mob, lawv lub hom phiaj thiab qhov tseem ceeb hauv lub neej hloov pauv. Paub seb koj qhov 'ib txwm tshiab' yog dab tsi tuaj yeem siv sijhawm thiab ntxhov siab. Kev cia siab ntawm koj tsev neeg thiab cov phooj ywg yuav txawv rau koj li. Koj tuaj yeem xav tias nyob ib leeg, qaug zog lossis muaj ntau tus cwj pwm txawv uas tuaj yeem hloov pauv txhua hnub.

Lub hom phiaj tseem ceeb tom qab kev kho mob rau koj cov lymphoma yog kom rov tau txoj sia thiab:            

  • ua kom nquag plias li sai tau hauv koj txoj haujlwm, tsev neeg, thiab lwm yam haujlwm hauv lub neej
  • txo cov kev mob tshwm sim thiab cov tsos mob ntawm tus mob qog noj ntshav thiab nws txoj kev kho mob      
  • txheeb xyuas thiab tswj cov kev mob tshwm sim lig      
  • pab kom koj muaj kev ywj pheej raws li qhov ua tau
  • txhim kho koj lub neej zoo thiab tswj kev puas siab puas ntsws zoo

Muaj ntau hom kev kho mob qog noj ntshav tuaj yeem pom zoo rau koj. Qhov no tuaj yeem txhais tau tias muaj ntau yam ntawm cov kev pabcuam xws li:     

  • kev kho lub cev, kev kho mob      
  • kev npaj noj haus thiab kev tawm dag zog      
  • kev xav, kev paub txog kev ua haujlwm thiab nyiaj txiag. 

Ntsiab lus

  • Primary Central Nervous System Lymphoma (PCNSL) yog ib qib siab aggressive subtype ntawm Non-Hodgkin Lymphoma uas yog tsim nyob rau hauv koj lub hauv paus paj hlwb (CNS).
  • PCNSL feem ntau tsis kis tawm sab nraud ntawm CNS tab sis tuaj yeem kis mus rau cov qog ntshav hauv cov txiv neej.
  • PCNSL txawv ntawm lymphomas uas pib lwm qhov hauv lub cev thiab kis mus rau CNS (secondary CNS lymphoma) thiab yuav tsum tau kho qhov sib txawv.
  • Cov tsos mob ntawm PCNSL muaj feem xyuam rau qhov chaw ntawm lymphoma, nrog rau cov tsos mob ntsig txog kev ua haujlwm ntawm koj lub hlwb, qaum qaum thiab ob lub qhov muag.
  • Muaj ntau ntau yam kev sim uas koj yuav tsum tau kuaj xyuas PCNSL, thiab cov no yuav suav nrog cov txheej txheem uas koj tau txais kev kho mob dav dav lossis hauv zos.
  • Kev kho mob rau PCNSL yog txawv los ntawm lwm yam subtypes ntawm lymphoma vim tias cov tshuaj yuav tsum dhau los ntawm koj cov ntshav-hlwb barrier mus rau lymphoma.
  • Cov tsos mob yuav siv sij hawm ib ntus los txhim kho tom qab kev kho mob vim qhov kev loj hlob qeeb ntawm cov paj hlwb, tab sis lwm cov tsos mob tuaj yeem txhim kho sai.
  • Tham nrog koj tus kws kho mob txog koj txoj kev pheej hmoo ntawm kev kho mob thiab dab tsi xav tau los ntawm koj txoj kev kho mob.
  • Koj tsis nyob ib leeg. Yog tias koj xav nrog ib tus kws saib xyuas mob qog nqaij hlav lymphoma tham txog koj cov qog ntshav qog ntshav, kev kho mob thiab cov kev xaiv nyem nyem lub pob Hu rau peb hauv qab ntawm qhov screen.

Kev txhawb nqa thiab cov ntaub ntawv

Kawm ntxiv txog koj cov kev kuaj ntshav ntawm no – Lab xeem online

Kawm ntxiv txog koj cov kev kho mob ntawm no - eviQ kev kho mob qog noj ntshav - Lymphoma

Nrhiav tawm Ntau

Sau npe rau tsab ntawv xov xwm

qhia no

Cov Ntawv Xov Xwm Sau Npe

Hu rau Lymphoma Australia Hnub no!

Thov nco ntsoov: Lymphoma Australia cov neeg ua haujlwm tsuas yog tuaj yeem teb rau emails xa ua lus Askiv xwb.

Rau cov neeg nyob hauv Australia, peb tuaj yeem muab kev pabcuam txhais lus hauv xov tooj. Kom koj tus nais maum lossis tus txheeb ze hais lus Askiv hu rau peb los npaj qhov no.