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Mitundu ina ya Lymphoma

Dinani apa kuti muwone mitundu ina ya lymphoma

Pulayimale Central Nervous System Lymphoma (PCNSL)

Primary central nervous system lymphoma, yofupikitsidwa ngati PCNSL, ndi yachilendo, yaukali (yomwe ikukula mofulumira) ya non-Hodgkin lymphoma (NHL), yomwe imayambira mu ubongo ndi / kapena msana. Zimapezeka kwambiri mwa anthu azaka zapakati pa 50 ndi 60 koma zimatha kuchitika pazaka zilizonse.

Ndizofala kwambiri kuti PCNSL ikhale mu ubongo wanu, koma ikhoza kukhala m'dera lililonse la CNS yanu. Pafupifupi chotupa chimodzi mwa 1 muubongo ndi mtundu wa CNS lymphoma.

Kuphulika kwa lumbar kungagwiritsidwe ntchito kufufuza lymphoma m'kati mwa mitsempha yanu, kapena kupereka mankhwala a chemotherapy mu ubongo wanu wa msana.

Lymphoma ndi khansa ya maselo oyera a magazi otchedwa lymphocytes ndipo akhoza kutchulidwa ngati mtundu wa Hodgkin, kapena Non-Hodgkin Lymphoma. Primary central nervous system lymphoma (PCNSL) ndi mtundu wosowa, waukali wa Non-Hodgkin Lymphoma yomwe imapezeka m'kati mwa mitsempha yanu (CNS) yomwe imaphatikizapo ubongo wanu, msana ndi maso. Ma lymphocyte a khansa mu PCNSL amatchedwa B-cell lymphocytes.

Tsambali likupatsani chidziwitso chomwe mukufuna ngati mukukumana ndi zizindikiro zilizonse, mukupeza matenda, kuyamba kulandira chithandizo cha PCNSL, kapena kukhala ndi zotsatira zoyipa zomwe zimagwirizanitsidwa ndi chithandizo cha PCNSL.

Patsambali:

Primary central nervous system lymphoma (PCNSL) fact sheet PDF

Chithunzi cha PCNSL

PCNSL imayamba pamene khansa ya B-cell lymphocytes (B-cell) imapanga mu minofu ya ubongo ndi / kapena msana. PCNSL ikhoza kuyambanso mu zigawo zomwe zimapanga chophimba chakunja cha ubongo (meninges) kapena m'maso (ocular lymphoma). 

Nthawi zina lymphoma imatha kufalikira kumadera ena a thupi ndikufalikira ku CNS. Izi ndizosiyana ndi PCNSL ndipo zimachitidwanso mosiyana. Ngati yayamba kunja kwa CNS ndikufalikira ku CNS imatchedwa secondary CNS lymphoma.

Chifukwa cha PCNSL sichidziwika monga momwe zimakhalira ndi ma lymphoma ambiri. Anthu amatha kukhudzidwa kwambiri ndi zaka zapakati pa 50 mpaka 60, ndi zaka zakubadwa zapakati pazaka 60, komabe zimatha kuchitika pazaka zilizonse. PCNSL imakhalanso yofala kwambiri mwa anthu omwe ali ndi chitetezo chamthupi chofooka, chomwe chingayambitsidwe ndi:

  • HIV (human immunodeficiency virus) matenda - izi ndizochepa tsopano chifukwa cha kupezeka kwa mankhwala oletsa tizilombo toyambitsa matenda.
  • Mankhwala - amene amagwiritsidwa ntchito kupondereza chitetezo cha m'thupi, monga pambuyo kumuika chiwalo kapena mitundu ina ya immunosuppressive mikhalidwe autoimmune monga nyamakazi.

Kodi PCNSL ingachiritsidwe?

Ma lymphoma ambiri owopsa amatha kuyankha bwino chithandizo chamankhwala chamankhwala chifukwa chemotherapy imagwira ntchito popha maselo omwe akukula mwachangu. Pali zinthu zambiri, komabe, zomwe zimakhudza ngati mudzachiritsidwa ku lymphoma yanu kapena ayi. Anthu ambiri akhoza kuchiritsidwa, ena akhoza kukhala ndi nthawi yachikhululukiro - pamene palibe chizindikiro cha lymphoma yomwe yatsala m'thupi mwanu, koma imatha kubwereranso (kubwerera) ndikusowa chithandizo china.

Kuti mudziwe zambiri za mwayi wanu wochiritsidwa, lankhulani ndi dokotala wanu wa magazi kapena oncologist.

Kodi Central Nervous System (CNS) imachita chiyani?

The dongosolo lalikulu la mitsempha (CNS) ndi mbali ya thupi lathu imene imayendetsa ntchito zonse za thupi lathu. Zimaphatikizapo ubongo, msana ndi maso.

Ubongo

Ubongo wathu umapangidwa ndi:

  • Cerebrum - izi zimayang'anira malankhulidwe athu ndi kumvetsetsa kwathu, zomverera zathu ndi kuyenda mwaufulu (mayendedwe omwe tasankha kupanga)
  • Cerebellum - imathandizira mayendedwe ndikuwongolera moyenera
  • Ubongo - imayendetsa ntchito zofunika za thupi, monga kupuma kwathu, kugunda kwa mtima ndi kuthamanga kwa magazi

Msana

Msana wathu umayenda kuchokera ku ubongo kutsika kumbuyo kwathu mkati mwa mafupa a msana. Mitsempha ingapo imalumikizana mwachindunji pa msana. Mitsempha imanyamula chidziwitso chokhudza kumva kuchokera kuzungulira thupi ndikunyamula mauthenga kupita ndi kuchokera ku ubongo kupita ku thupi lathu lonse, kulamulira minofu yathu, ndi ntchito zonse za thupi lathu.

Kodi CNS yathu imatetezedwa bwanji?

CNS yathu imasiyanitsidwa ndi thupi lathu lonse ndikutetezedwa ku zoopsa, matenda ndi matenda m'njira zingapo.

  • The meninges ndi zigawo zoteteza za minofu yomwe imaphimba ubongo ndi msana - izi ndizomwe zimayaka mu 'meningitis'.
  • A madzimadzi apadera amatchedwa 'cerebrospinal fluid'(CSF) imazungulira ubongo ndi msana kuti iwatseke - imapezeka pakati pa ma meninges ndi ubongo ndi msana.
  • The chotchinga magazi ndi ubongo zimazungulira ubongo wathu - ndi chotchinga cha maselo ndi mitsempha yamagazi yomwe imalola kuti zinthu zina zifike ku ubongo. Izi zimateteza ku mankhwala owopsa ndi matenda, komanso zimalepheretsa kapena kusokoneza mankhwala ambiri a chemotherapy omwe amachoka m'magazi kupita ku ubongo.
Kuti mumvetse PCNSL muyenera kudziwa pang'ono za ma lymphocyte anu a B-Cell.

B-cell lymphocytes:

  • Ndi mtundu wa maselo oyera a magazi
  • Menyani matenda ndi matenda kuti mukhale athanzi. 
  • Kumbukirani matenda omwe mudakhala nawo m'mbuyomu, kotero ngati mutatenganso matenda omwewo, chitetezo chamthupi chanu chingathe kulimbana nacho moyenera komanso mwachangu. 
  • Amapangidwa m'mafupa anu (gawo la spongy pakati pa mafupa anu), koma nthawi zambiri amakhala m'mitsempha yanu yomwe imaphatikizapo: 
  1. ma lymph node
  2. mitsempha ya lymphatic ndi madzimadzi amadzimadzi
  3. ziwalo - ndulu, thymus, tonsils, appendix
  4. minofu ya lymphoid
  • Mutha kuyenda kudzera m'mitsempha yanu kupita ku gawo lililonse la thupi lanu kukalimbana ndi matenda kapena matenda. 
Ma lymphatic system ndi gawo la chitetezo cha mthupi ndipo amakusungani wathanzi polimbana ndi majeremusi. Zimaphatikizapo ma lymph nodes, mitsempha yamagazi ndi ziwalo monga ndulu yanu, thymus ndi zina. Anu B-cell lymphocytes amakhala makamaka mu lymphatic system yanu.
Kodi chimachitika ndi chiyani PCNSL ikayamba?

PCNSL imayamba pamene ma lymphocyte a khansa amapezeka m'kati mwa mitsempha yanu (CNS), yomwe imaphatikizapo ubongo wanu, msana, maso, mitsempha ya cranial ndi chitetezo cha minofu yomwe imaphimba ubongo wanu ndi msana wanu wotchedwa meninges.

Mukakhala ndi PCNSL, ma lymphocyte anu a khansa:

  • Kukula mosalamulirika
  • Sizigwira ntchito moyenera polimbana ndi matenda ndi matenda
  • Zitha kukhala zazikulu kuposa momwe ziyenera kukhalira ndipo zimatha kuwoneka mosiyana ndi ma B-maselo anu athanzi 
  • Zingayambitse lymphoma kukula mu ubongo wanu, msana ndi maso.
  • Chifukwa cha zotchinga zotetezera kuzungulira CNS yathu, PCNSL sichimafalikira ku ziwalo zina za thupi lanu monga mitundu ina ya lymphoma ingatheke, nthawi zina imatha kufalitsa ma testes mwa amuna.

Zizindikiro pamene lymphoma ili mu Central Nervous System (CNS)

Zizindikiro za lymphoma mu CNS yanu zimagwirizana ndi ntchito za ubongo wanu, maso ndi msana. Zitengera gawo la CNS yanu lomwe lakhudzidwa ndipo zingaphatikizepo izi:

  • litsipa
  • kusintha kwa masomphenya anu
  • chisokonezo kapena kusintha kukumbukira
  • kusintha kwa chidziwitso (kugona ndi kusalabadira)
  • kuvutika kulankhula kapena kumeza
  • kusintha kwa maganizo kapena umunthu wanu
  • kukomoka (kukomoka)
  • kunyoza ndi kusanza
  • kusowa chilakolako (osafuna kudya) ndi kuwonda
  • kuvutika kupita kuchimbudzi
  • kuvutika kuyenda, kusakhazikika kapena kugwa
  • kufooka, dzanzi kapena kumva kulasalasa.

Kuzindikira, kuyika ndi kuyika kwa PCNSL

Ngati dokotala akukayikira kuti muli ndi lymphoma muyenera kuyesedwa kangapo. Mosiyana ndi ma subtypes a lymphoma, masitepe samachitika ngati muli ndi PCNSL chifukwa lymphoma imangokhala pakatikati pa mitsempha yanu (CNS). Kufalikira kulikonse kunja kwa CNS nthawi zambiri kumakhala mwa amuna okha komanso kuma testes okha. 

PCNSL nthawi zonse imatengedwa ngati lymphoma yapamwamba kutanthauza kuti ndi yaukali. Imakula mwachangu ndipo imatha kudutsa mu CNS yanu mwachangu. Ma cell a khansa (ma cell a lymphoma) amaonekanso mosiyana kwambiri ndi ma B-cell anu athanzi chifukwa amakula mwachangu ndipo alibe nthawi yoti apange bwino.

Dinani pamutu womwe uli pansipa kuti mudziwe zambiri za mtundu wa mayeso omwe mungafunike kuwazindikira, ndikuphunzira zambiri za PCNSL yanu.

Chimake

Kuti muzindikire PCNSL mudzafunika biopsy. Biopsy ndi njira yochotsera gawo, kapena ma lymph node omwe akhudzidwa kapena minofu yomwe yakhudzidwa. Pa nthawi ya opaleshoniyo mutha kupatsidwa mankhwala opha ululu wamba kapena wamba kuti mukhale omasuka, kapena kuwonetsetsa kuti simuli maso mukamaliza.

Mtundu wa biopsy woti uchitidwe umadalira kumene lymphoma ili.

Ngati lymphoma imaganiziridwa kuti ili mwanu:

  • Ubongo - katswiri wa opaleshoni ya ubongo (katswiri wofufuza ndi kuchiza mavuto ndi CNS) amatenga ubongo wa ubongo. Ziphuphu (kapena zitsanzo za zotupa) mkati mwa ubongo wanu zidzachotsedwa pogwiritsa ntchito CT scan kuti zithandize kutsogolera singano ya biopsy kumalo oyenera. Izi zimatchedwa a 'stereotactic biopsy'. Mudzakhala ndi mankhwala oletsa kupweteka kwa njirayi chifukwa ndikofunikira kuti musasunthe.
  • Diso - katswiri wa ophthalmologist (katswiri wa matenda ndi kuvulala kwa diso) angatenge pang'ono za vitreous (zofanana ndi gel mkati mwa diso lanu) kuti ayang'ane maselo a lymphoma.
  • Msana - katswiri wa radiologist akhoza kutenga biopsy kuchokera ku msana wanu.

Mayeso a magazi

Kuyezetsa magazi kumayesedwanso poyesa kufufuza lymphoma yanu, komanso panthawi yonse ya chithandizo kuti adokotala amvetse bwino za thanzi lanu lonse, ndikuwonetsetsa kuti ziwalo zanu zikugwira ntchito bwino kuti mupirire chithandizo.

Kujambula uku nthawi zambiri kumapereka zithunzi zabwino kwambiri zaubongo wanu ndi mbali zina za CNS komanso zimatha kuzindikira kupsinjika kwa msana.

MRI
MRI scan ya ubongo

Kujambula uku kumachitika kuti azindikire lymphoma kwina kulikonse m'thupi. Amapereka zithunzi zatsatanetsatane zomwe zimapereka zambiri kuposa X-ray wamba. Akhozanso kuchitidwa kuti ayang'ane mafupa omwe ali pamsana wanu.

CT scan

Kujambula kwamtunduwu nthawi zambiri kumagwiritsidwa ntchito limodzi ndi CT scan kuti muzindikire lymphoma yogwira ntchito kwina kulikonse m'thupi lanu. Zimatengera chithunzi cha mkati mwa thupi lanu lonse. Mudzapatsidwa singano yokhala ndi mankhwala omwe maselo a khansa monga maselo a lymphoma, amamwa. Mankhwalawa amathandiza PET scan kuti izindikire kumene lymphoma ili ndi kukula kwake ndi mawonekedwe ake powunikira malo omwe ali ndi maselo a lymphoma. Izi nthawi zina zimatchedwa "zotentha".  

Monga PCNSL ingakhudze maso mungafunikenso mayesero osiyanasiyana a maso. Katswiri wa maso (katswiri wa maso) adzagwiritsa ntchito ophthalmoscope - chida chokhala ndi lens yowala komanso yaying'ono yokulitsa - kuti muwone bwino mkati mwa diso lanu. Mayesero ena oyerekeza amatha kuchitidwa ndipo izi zimathandiza dokotala wamaso kuyang'ana chotupacho komanso kuwona ngati khansa yafalikira.

 

Biopsy ya diso ingafunike. Izi zimatchedwa vitrectomy. Kachida kakang'ono kamalowetsedwa m'diso ndipo pamatenga zitsanzo za jelly-like vitreous, yomwe ndi chinthu chomwe chimadzaza pakati pa diso.

Ma testicular ultrasound kwa amuna ndi mayeso omwe amapeza zithunzi za ma testicles ndi minyewa yozungulira mu scrotum. Ultrasound iyi ikhoza kuchitidwa monga PCNSL ina imatha kufalikira ku ma testes.

Results

Kudikirira kuti zotsatira zanu zonse zibwere kungakhale nthawi yovuta kwambiri kwa inu ndi okondedwa anu. Ndikofunika kulankhula za momwe mukumvera komanso kukhala omasuka ndi omwe akuzungulirani pazomwe mukufuna. Anthu ambiri amafuna kukuthandizani, koma sadziwa momwe mungawadziwitse zomwe mukufunikira, mutha kuwathandiza kuti akuthandizeni.

Zingakuthandizeninso kuyamba kukonzekera zomwe mungafunike m'miyezi ikubwerayi ngati mukufuna kulandira chithandizo. Tayika maupangiri pa tsamba lathu la Living with Lymphoma - The Practical Stuff. Dinani ulalo womwe uli pansipa kuti muwongoleredwe patsambalo.

Mutha kulumikizananso Namwino Wathu Wachidziwitso kuti mulankhule ndi m'modzi mwa Anamwino Osamalira Lymphoma. Ingodinani batani la Lumikizanani nafe pansi pa tsambali.

Mukhozanso kujowina imodzi mwamasamba athu ochezera a pa Intaneti kuti mucheze ndi anthu ena okhala nawo. Lumikizanani ndi masamba athu ochezera pa intaneti podina maulalo omwe ali pamwamba pa tsambalo.

Kuti mumve zambiri onani
Kukhala ndi Lymphoma - Zinthu Zothandiza

Chithandizo cha PCNSL

Kukhala ndi chidziwitso choyenera kungakuthandizeni kudzidalira komanso kudziwa zomwe mungayembekezere, komanso kungakuthandizeni kukonzekera zomwe mungafunike. Koma zingakhale zovuta kudziwa mafunso oti mufunse pamene mukuyamba kulandira chithandizo. Ngati simukudziwa, zomwe simudziwa, mungadziwe bwanji zomwe mungafunse?

Talemba mndandanda wa mafunso omwe mungawapeze kukhala othandiza. Zoonadi, mkhalidwe wa aliyense ngwosiyana, chotero mafunso ameneŵa samakhudza chirichonse, koma amapereka chiyambi chabwino. Dinani ulalo womwe uli pansipa kuti mupeze kopi ya PDF yomwe mutha kutsitsa ndikusindikiza ngati mukufuna.

Dinani apa kuti mutsitse Mafunso kuti mufunse dokotala musanayambe chithandizo.

Kuteteza chonde

Kaya ndinu mwamuna kapena mkazi, mankhwala ambiri oletsa khansa amatha kusokoneza chonde chanu - kuthekera kwanu kopanga ana. Ngati mukufuna kukhala ndi ana mutalandira chithandizo, kapena simukudziwa ngati mungatero, lankhulani ndi dokotala wanu za zomwe mungachite kuti muteteze kubereka kwanu panthawi ya chithandizo.

Mwachidule mitundu yamankhwala

Dinani pazithunzi pansipa kuti muwone mwachidule mitundu yosiyanasiyana yamankhwala yomwe mungapatsidwe pochiza PCNSL yanu.

Chithandizo cha Steroid
Mutha kuyambika pa ma steroid mukakhala ndi ma biopsies anu. Steroids amathandizira kuchepetsa kutupa kuzungulira malo a lymphoma ndipo angathandize kusintha zizindikiro zanu. Nthawi zambiri amayamba pambuyo pa biopsies chifukwa lymphoma imatha kukhala yovuta kudziwa ngati ma steroid aperekedwa kale.

Komabe, ngati muli ndi zizindikiro zoopsa ndipo dokotala wanu ali ndi chidaliro kuti muli ndi PCNSL, akhoza kusankha kuyamba ma steroids kuti athetse zizindikiro zanu ngakhale musanayambe biopsy.

Steroids amakhalanso poizoni ku maselo a lymphoma kotero amatha kuthandizira kuchepetsa lymphoma pamene akudikirira kuti chithandizo china chiyambe.

Steroids atha kuperekedwa kudzera m'mitsempha (kudzera mumtsempha) kapena pakamwa (pakamwa). Steroid wamba ndi dexamethasone.
Chemotherapy (Chemotherapy)
Mutha kumwa mankhwalawa ngati piritsi kapena kuperekedwa ngati dontho (kulowetsedwa) mumtsempha wanu (m'magazi anu) ku chipatala cha khansa kapena chipatala. Chemo imapha maselo omwe amakula mwachangu kotero imakhala yogwira mtima motsutsana ndi ma lymphomas aukali, komanso imatha kukhudza ena mwama cell anu abwino omwe amakula mwachangu, zomwe zimayambitsa zotsatira zosafunika.

Chemo yomwe mumapeza ya PCNSL ikhoza kukhala yosiyana ndi anthu omwe ali ndi mitundu ina ya lymphoma, chifukwa mankhwala amafunika kudutsa chotchinga cha ubongo wanu kuti apite ku lymphoma yanu. Ndizofala kukhala ndi chemotherapy ndi immunotherapy monga rituximab.
Mankhwala a monoclonal
Ma antibodies a monoclonal nthawi zina amatchedwa immunotherapy chifukwa amathandiza chitetezo chanu cha mthupi kuzindikira ndikumenyana ndi lymphoma.

Mutha kukhala ndi kulowetsedwa kwa MAB ku chipatala cha khansa kapena chipatala. Ma MAB amamatira ku cell ya lymphoma ndikukopa matenda ena olimbana ndi maselo oyera amagazi ndi mapuloteni ku khansa kuti chitetezo chanu cha mthupi chitha kulimbana ndi PCNSL.
Chithandizo cha Magetsi
Radiotherapy imagwiritsa ntchito radiation kupha maselo a khansa. Zili ngati ma X-ray amphamvu kwambiri ndipo amachitidwa tsiku lililonse, nthawi zambiri kuyambira Lolemba mpaka Lachisanu kwa milungu ingapo.

Radiotherapy yaubongo wonse imagwiritsidwa ntchito ngati chithandizo chophatikiza pambuyo pa chemotherapy.

Mpaka pakati pa zaka za m'ma nineties anali chithandizo chachikulu cha PCNSL, komabe tsopano amaperekedwa pamodzi ndi chemotherapy. Thandizo lophatikizira likufuna kuchepetsa chiopsezo choyambiranso (kubwerera kwa lymphoma). Radiotherapy ingagwiritsidwe ntchito yokha ngati simungathe kulekerera mankhwala amphamvu.
Kupanga khungu la tsinde
Ngati ndinu wamng'ono ndipo muli ndi lymphoma yoopsa, SCT ikhoza kulangizidwa ngati chithandizo, ngakhale kuti mankhwalawa sali oyenera kwa aliyense.

SCT imachitidwa kuti m'malo mwa mafupa anu odwala ndi maselo atsopano omwe amatha kukula kukhala maselo athanzi amagazi. Ndi SCT, tsinde maselo amachotsedwa m'magazi. Ma cell stem amatha kuchotsedwa kwa wopereka kapena kusonkhanitsidwa kuchokera kwa inu mutalandira chemotherapy.

Ngati tsinde maselo amachokera kwa wopereka, amatchedwa allogeneic stem cell transplant. Ngati ma tsinde anu asonkhanitsidwa, amatchedwa autologous stem cell transplant.
Slide yam'mbuyo
Slide yotsatira

Chithandizo choyamba

Muyenera kuyamba kulandira chithandizo posachedwa zotsatira zanu zonse zikabwera. Nthawi zina, mutha kuyamba zotsatira zonse zoyezetsa zisanalowe. Zitha kukhala zochulukira mukayamba kulandira chithandizo. Mungakhale ndi maganizo ambiri okhudza mmene mungapiririre, mmene mungasamalire kunyumba, kapena mmene mungadwalire.

Adziwitseni gulu lanu lachipatala ngati mukuwona kuti mungafunike chithandizo chowonjezera. Atha kukuthandizani pokuitanani kuti mukakumane ndi wothandiza anthu kapena akatswiri ena azaumoyo kuti akuthandizeni kuthana ndi zovuta zatsiku ndi tsiku zomwe mungakumane nazo. Mukhozanso kufikira kwa Anamwino Osamalira Lymphoma podina batani la "Lumikizanani nafe" pansi pa tsamba lino.

Mukayamba kumwa mankhwala koyamba, amatchedwa 'mankhwala oyamba'. Mutha kukhala ndi mankhwala opitilira umodzi, ndipo izi zingaphatikizepo radiotherapy, chemotherapy kapena antibody monoclonal.

Chithandizo chodziwika bwino cha mzere woyamba chitha kukhala:

 Mlingo wambiri wa methotrexate 

Izi zitha kuphatikizidwa ndi kapena popanda monoclonal antibody, rituximab.

 MATRix

Uku ndi kuphatikiza kwa mankhwala osiyanasiyana a chemotherapy ndi antibody monoclonal - methotrexate, cytarabine, thiotepa ndi rituximab - pa PCNSL yomwe yangopezeka kumene.

R-MPV (Gawo loyamba ndi Gawo lachiwiri)

Gawo loyamba - Monoclonal antibody (rituximab) ndi kuphatikiza kwa chemotherapy kuphatikizapo methotrexate, procarbazine ndi vincristine.

Gawo lachiwiri - Mankhwala amphamvu kwambiri a chemotherapy - cytarabine

Methotrexate ndi cytarabine

Kuphatikiza kwa ma chemotherapies awiri a PCNSL omwe angopezeka kumene.

Mankhwala otchedwa intrathecal chemotherapy

Awa ndi chemotherapy omwe amaperekedwa mumadzi am'mimba mwa njira yoboola m'chiuno. Izi zimachitika ngati lymphoma imapezeka mumsana wanu.

Kutenga nawo gawo pazachipatala

Izi zingaphatikizepo mayesero azachipatala okhudzana ndi njira zochizira ndi zina. Funsani dokotala wanu ngati mukuyenerera kuyesedwa kwachipatala koyamba.

Radiotherapy kapena Stem Cell Transplant

Ngati lymphoma iyankha ku chemotherapy, gulu lanu lachipatala lingakupatseni radiotherapy yaubongo wonse kapena chithandizo chamankhwala autologous stem cell transplant (onani pamwambapa). Awa ndi mankhwala ophatikizika, kutanthauza kuti amagwiritsidwa ntchito kuchepetsa chiopsezo choyambiranso pambuyo pochiza bwino.

Chithandizo chachiwiri komanso chopitilira

Ngati CNS lymphoma yanu ibwereranso (kubwerera) kapena ikukaniza (sikuyankha) kuchipatala, pangakhale mankhwala ena omwe alipo.

Chithandizo chomwe muli nacho mukayambiranso kapena kukhala ndi PCNSL yopumira imatchedwa chithandizo chamzere wachiwiri. Mankhwalawa amatengera momwe muliri panthawiyo, chithandizo chomwe mwalandira kale komanso momwe lymphoma ikukukhudzani. Katswiri wanu akhoza kukuuzani zomwe mungasankhe, zomwe zingaphatikizepo:

  • Chithandizo champhamvu kwambiri (champhamvu) cha chemotherapy, mwina chotsatiridwa ndi autologous stem cell transplant (osayenera kwa anthu ena).
  • Radiotherapy - ngati sichinapatsidwe kale.
  • Chithandizo chapalliative choperekedwa ndi cholinga chochepetsa zizindikiro.
  • Kutenga nawo gawo pazachipatala.

chipatala Mayesero

Ndibwino kuti nthawi iliyonse yomwe mukufuna kuyamba mankhwala atsopano mumafunsa dokotala za mayesero a zachipatala omwe mungakhale oyenerera.

Mayesero azachipatala ndi njira yofunikira yopezera mankhwala atsopano, kapena kusakanizidwa kwamankhwala kuti mupititse patsogolo chithandizo cha PCNSL mtsogolo. Akhozanso kukupatsani mwayi woyesera mankhwala atsopano, mankhwala osakaniza kapena mankhwala ena omwe simungathe kupita nawo kunja kwa mayesero. Ngati mukufuna kutenga nawo mbali pamayesero azachipatala, funsani dokotala kuti ndi mayesero ati azachipatala omwe mukuyenera nawo. 

Pali machiritso ambiri ndi kuphatikiza kwatsopano kwamankhwala komwe akuyesedwa pano m'mayesero azachipatala padziko lonse lapansi kwa anthu omwe ali ndi PCNSL yomwe yangopezeka kumene komanso yoyambiranso/yokana. Njira zina zochiritsira zomwe zikufufuzidwa ndi:

  • Ibrutinib (Imbruvica®)
  • Zanubrutinib (Brukinsa®) ndi Tiselizumab
  • Pembrolizumab (Keytruda®)
  • GB5121 - choletsa cha BTK cholowera muubongo
Kuti mumve zambiri onani
Zotsatira za mankhwala

Kumvetsetsa mayesero azachipatala

Zotsatira za PCNSL

Kuneneratu ndi mawu omwe amagwiritsidwa ntchito pofotokoza njira yomwe ingatheke matenda anu, momwe angayankhire chithandizo ndi momwe mungachitire panthawi ya chithandizo ndi pambuyo pake.

Pali zinthu zambiri zomwe zimapangitsa kuti mukhale ndi matenda anu ndipo sizingatheke kufotokoza zonse zokhudzana ndi matenda.

Zinthu zomwe zingakhudze prognosis

 Zina mwazinthu zomwe zingakhudze kuneneratu kwanu ndi izi:

  • Zaka zanu ndi thanzi lanu lonse panthawi ya matenda
  • Momwe mumayankhira chithandizo

Nthawi zina zizindikiro za CNS lymphoma zimatha msanga ndi chithandizo. Kuchiza koyamba ndi ma steroids kungakhale kothandiza kwambiri pochotsa zizindikiro. Komabe, minyewa imakula pang'onopang'ono, ndipo nthawi zina zimatenga nthawi kuti zizindikiro zisinthe. Ena a inu mutha kuwona kusintha kwapang'onopang'ono kwazizindikiro, ena atha kupeza kuti zizindikiro sizingathetsedwe, makamaka ngati analipo asanalandire chithandizo.

Kupeza chithandizo

Gulu lanu lachipatala likhoza kuthandizira kuchira kwanu potumiza kwa akatswiri oyenerera. Ngati mukumva kufooka kwa minofu ndi kutaya mphamvu kapena simukuchira msanga, muyenera kuganizira zowonana ndi physiotherapist ndi / kapena occupational therapist momwe angapereke chithandizo ndi uphungu kuti mukhale ndi moyo wabwino. Thandizo lawo lingathenso kuletsa zizindikiro kuti zisamapitirire kukulirakulira kapena mavuto ena omwe amakula pakapita nthawi.

Akatswiri a zamaganizo angapereke chithandizo ngati pali zovuta zamaganizo (zoganiza), monga kukumbukira kapena kusamala. Akatswiri a zamaganizo ndi alangizi angathandizenso ndi momwe lymphoma yanu imakhudzira.

Ndikofunika kuzindikira kuti njira zothandizira PCNSL zakhala zikuyenda bwino kwambiri m'zaka zaposachedwa. Komabe, PCNSL ikhoza kukhala yovuta kuchiza, ndipo mankhwala ena ali ndi chiopsezo choyambitsa mavuto a nthawi yaitali a ubongo (mavuto ndi ubongo ndi maso). Mavutowa amakhala ochuluka ngati mutapezeka ndi CNS lymphoma mutakula.  

 

Kupulumuka - Kukhala ndi, komanso pambuyo pa khansa

Kukhala ndi moyo wathanzi, kapena kusintha kwa moyo wabwino mukalandira chithandizo kungathandize kwambiri kuti muchiritsidwe. Pali zinthu zambiri zomwe mungachite kuti mukhale ndi moyo wabwino pambuyo pa Burkitt. 

Anthu ambiri amapeza kuti atapezeka ndi khansa, kapena kulandira chithandizo, zolinga zawo ndi zomwe amaika patsogolo pamoyo wawo zimasintha. Kudziwa ‘zachilendo’ zanu kungatenge nthawi komanso kukukhumudwitsani. Zoyembekeza za banja lanu ndi anzanu zingakhale zosiyana ndi zanu. Mutha kudzimva kukhala osungulumwa, kutopa kapena kuchuluka kwa malingaliro osiyanasiyana omwe angasinthe tsiku lililonse.

Zolinga zazikulu pambuyo pa chithandizo cha lymphoma yanu ndi kukhalanso ndi moyo ndipo:            

  • khalani okangalika momwe mungathere pantchito yanu, banja lanu, ndi maudindo ena amoyo wanu
  • kuchepetsa zotsatira ndi zizindikiro za khansa ndi chithandizo chake      
  • zindikirani ndikuwongolera zovuta zilizonse mochedwa      
  • kukuthandizani kuti mukhale odziyimira pawokha momwe mungathere
  • sinthani moyo wanu komanso kukhala ndi thanzi labwino

Mitundu yosiyanasiyana ya kukonzanso khansa ikhoza kulangizidwa kwa inu. Izi zitha kutanthauza chilichonse chamitundumitundu za mautumiki monga:     

  • chithandizo chamankhwala, kusamalira ululu      
  • kukonza zakudya ndi masewera olimbitsa thupi      
  • uphungu wamalingaliro, ntchito ndi zachuma. 

Chidule

  • Primary Central Nervous System Lymphoma (PCNSL) ndi gawo laling'ono la Non-Hodgkin Lymphoma lomwe limayamba m'katikati mwa mitsempha yanu (CNS).
  • PCNSL sichimafalikira kunja kwa CNS koma imatha kufalikira ku ma testes mwa amuna.
  • PCNSL ndi yosiyana ndi ma lymphoma omwe amayamba kwina m'thupi ndikufalikira ku CNS (secondary CNS lymphoma) ndipo amafunika kuchitidwa mosiyana.
  • Zizindikiro za PCNSL zimagwirizana ndi malo a lymphoma, kuphatikizapo zizindikiro zokhudzana ndi ntchito za ubongo, msana ndi maso.
  • Pali mitundu ingapo yoyezetsa yomwe mungafunikire kuti muzindikire PCNSL, ndipo izi zingaphatikizepo njira zomwe mumapatsidwa mankhwala oletsa ululu wamba kapena wamba.
  • Kuchiza kwa PCNSL ndi kosiyana ndi mitundu ina ya lymphoma monga mankhwala amafunika kudutsa chotchinga mu ubongo wanu kuti apite ku lymphoma.
  • Zizindikiro zimatha kutenga nthawi kuti zisinthe pambuyo pa chithandizo chifukwa cha kukula pang'onopang'ono kwa maselo a mitsempha, koma zizindikiro zina zimatha kusintha mofulumira.
  • Lankhulani ndi dokotala wanu za mwayi wanu wochiritsidwa ndi zomwe mungayembekezere kuchokera ku chithandizo chanu.
  • Simuli nokha. Ngati mungafune kuyankhula ndi m'modzi mwa Anamwino Osamalira Ma Lymphoma za lymphoma yanu, chithandizo ndi zomwe mungachite dinani batani Lumikizanani pansi pazenera.

Thandizo ndi chidziwitso

Dziwani zambiri za kuyezetsa magazi anu apa - Mayeso a labu pa intaneti

Dziwani zambiri zamankhwala anu apa - eviQ mankhwala oletsa khansa - Lymphoma

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