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Mamwe Mhando dzeLymphoma

Dzvanya pano kuti uone mamwe marudzi e-lymphoma

Yekutanga Central Nervous System Lymphoma (PCNSL)

Primary central nervous system lymphoma, yakapfupikiswa sePCNSL, isingawanzoitiki, ine hutsinye (inokurumidza kukura) sub-type ye-non-Hodgkin lymphoma (NHL), inokura muuropi uye / kana musana. Inonyanya kuitika muvanhu vane makore ekuma50s ne60s asi inogona kuitika chero zera.

Izvo zvakajairika kuti PCNSL ive muuropi hwako, asi inogona kunge iri mune chero nzvimbo yeCNS yako. Around 1 mu50 brain tumors imhando yeCNS lymphoma.

A lumbar puncture inogona kushandiswa kutarisa lymphoma mukati mako tsinga system, kana kuendesa chemotherapy muuropi yako spinal fluid.

Lymphoma igomarara remasero machena eropa anonzi lymphocytes uye anogona kuverengerwa serudzi rweHodgkin, kana Non-Hodgkin Lymphoma. Primary central central nervous system lymphoma (PCNSL) imhando isingawanzo, ine hutsinye yeNon-Hodgkin Lymphoma inowanikwa mukati mako system system (CNS) iyo inosanganisira uropi hwako, musana uye maziso. Ma lymphocytes ane kenza muPCNSL anonzi B-cell lymphocytes.

Peji rino rewebhu rinokupa ruzivo rwaunoda kana uine chero zviratidzo nezviratidzo, muchirongwa chekuongororwa, kutanga kurapwa kwePCNSL, kana kuve nemhedzisiro inoenderana nekurapwa kwePCNSL.

Pane iri peji:

Primary central nervous system lymphoma (PCNSL) fact sheet PDF

Pfupiso yePCNSL

PCNSL inokura apo kenza yeB-cell lymphocytes (B-masero) inoumba mu lymphoid tissue yeuropi uye / kana musana. PCNSL inogonawo kutanga muzvikamu zvinoumba chifukidziro chekunze cheuropi (meninges) kana mumaziso (ocular lymphoma). 

Dzimwe nguva lymphoma inogona kutanga mune dzimwe nzvimbo dzemuviri uye inopararira kune CNS. Izvi zvinopesana nePCNSL uye zvinobatwa zvakasiyana zvakare. Kana yakatanga kunze kweCNS uye ichipararira kuCNS inonzi yechipiri CNS lymphoma.

Chikonzero chePCNSL hachizivikanwi sezvakaita ma lymphomas akawanda. Vanhu vanonyanya kukanganiswa pakati pemakore makumi mashanu kusvika makumi matanhatu emakore, neavhareji yezera rekuongororwa kutenderera makore makumi matanhatu, zvisinei zvinogona kuitika chero zera. PCNSL inowanikwawo zvishoma kune vanhu vane immune system isina simba, iyo inogona kukonzerwa ne:

  • Utachiona hweHIV (human immunodeficiency virus) - izvi hazvisati zvanyanya kuitika nekuda kwekuvapo kwemishonga inorwisa mavhairasi inoshanda.
  • Mishonga - iyo inoshandiswa kudzvanyirira immune system, sekunge mushure mekutapurirana nhengo kana mamwe marudzi emishonga yekudzivirira zvirwere zve autoimmune eg rheumatoid arthritis.

Ko PCNSL inorapika here?

Mazhinji ane hutsinye lymphomas anogona kupindura zvakanaka kurapwa nechemotherapy nekuti chemotherapy inoshanda nekuuraya masero anokurumidza kukura. Pane zvinhu zvakawanda zvakadaro, izvo zvinokanganisa kana iwe uchizoporeswa kubva kune yako lymphoma kana kwete. Vanhu vazhinji vanogona kurapwa, vamwe vanogona kunge vaine nguva yekuregererwa - uko pasina chiratidzo che lymphoma chasara mumuviri wako, asi zvino inogona kudzoka zvakare (kudzoka) uye inoda kumwe kurapwa.

Kuti uzive zvakawanda nezvemikana yako yekurapwa, taura nevehematologist wako kana oncologist.

Chii chinoitwa neCentral Nervous System (CNS)?

The yepakati tsinga system (CNS) inhengo yomuviri wedu inodzora mabasa edu ose emuviri. Zvinosanganisira uropi hwedu, musana uye maziso.

Uropi

Uropi hwedu hunoumbwa ne:

  • Cerebrum - izvi zvinotonga kutaura kwedu uye kunzwisisa, manzwiro edu uye kufamba kwekuzvidira (mafambiro atinosarudza kuita)
  • Cerebellum - inobatsira nekufamba uye inodzora chiyero chedu
  • Brainstem - inodzora mashandiro akakosha emuviri, sekufema kwedu, kurova kwemoyo uye BP

Muzongoza

Mutsipa wedu wemusana unomhanya kubva muuropi hwedu uchidzika kumashure kwedu mukati memapfupa emusana. Nhepfenyuro dzetsinga dzinobatana dzakananga kumusana. Tsinga dzinotakura ruzivo rwekunzwa kubva kumativi ese emuviri uye dzinotakura mameseji kuenda nekubva kuuropi hwedu kuenda kune yese yemuviri wedu, kudzora tsandanyama dzedu, uye ese emuviri wedu mabasa.

CNS yedu inodzivirirwa sei?

CNS yedu yakapatsanurwa kubva kune yese yemuviri wedu uye yakadzivirirwa kubva mukushungurudzika, kutapukirwa uye chirwere munzira dzakawanda.

  • The meninges zvidziviriro zvematishu zvinovhara uropi nemuzongoza - izvi ndizvo zvinopisa mu'meningitis'.
  • Mvura yakakosha inonzi 'cerebrospinal fluid'(CSF) inotenderedza huropi nemuzongoza kuti zvidzivise - inowanikwa munzvimbo iri pakati pemameninges nehuropi nemuzongoza.
  • The ropa-brain brain inotenderedza uropi hwedu - imhinganidzo yemasero nemidziyo yeropa inongobvumira zvimwe zvinhu kusvika kuuropi. Izvi zvinozvidzivirira kubva kumakemikari anokuvadza uye zvirwere, uye zvinodzivirira kana kukanganisa mishonga yakawanda yechemotherapy inopfuura kubva muropa ichienda kuuropi.
Kuti unzwisise PCNSL unofanirwa kuziva zvishoma nezveB-Cell lymphocytes yako.

B-Cell lymphocytes:

  • Imhando yemasero machena eropa
  • Rwisa utachiona nezvirwere kuti uchengetedze hutano. 
  • Rangarira utachiona hwawaiva nahwo munguva yakapfuura, saka kana ukawana utachiona humwe chetehwo zvakare, immune system yemuviri wako inogona kurwisa zvakanyanya uye nekukurumidza. 
  • Inogadzirwa mumwongo wako (iyo spongy chikamu pakati pemapfupa ako), asi kazhinji inogara mune yako lymphatic system inosanganisira yako: 
  1. lymph nodes
  2. lymphatic midziyo uye lymph fluid
  3. nhengo - spleen, thymus, tonsils, appendix
  4. lymphoid tishu
  • Inogona kufamba kuburikidza ne lymphatic system yako, kune chero chikamu chemuviri wako kurwisa hutachiona kana chirwere. 
Yako lymphatic system chikamu che immune system yako uye inokuchengetedza hutano nekurwisa utachiona. Inosanganisira lymph nodes yako, lymphatic midziyo uye nhengo dzakadai sepleen yako, thymus nezvimwe. Yako B-cell lymphocytes inorarama zvakanyanya mu lymphatic system yako.
Chii chinoitika kana PCNSL inokura?

PCNSL inokura apo kenza lymphocytes inowanikwa mukati mako mukati menheyo system (CNS), iyo inosanganisira uropi hwako, musana, maziso, cranial nerve uye inodzivirira yetishu inovhara uropi hwako uye musana wemusana unonzi meninges.

Paunenge uine PCNSL, yako kenza lymphocytes:

  • Kura zvisingadzoreki
  • Hazvishande zvinobudirira kurwisa hutachiona uye zvirwere
  • Inogona kuva yakakura kupfuura yavanofanira uye inogona kutaridzika zvakasiyana kune ako ane hutano B-masero 
  • Inogona kukonzera lymphoma kukura muuropi hwako, musana uye maziso.
  • Nekuda kwezvipingamupinyi zvinodzivirira zvakatenderedza CNS yedu, PCNSL haiwanzo kupararira kune dzimwe nhengo dzemuviri wako semamwe marudzi e lymphoma anogona zvakadaro, anogona dzimwe nguva kuparadzira testes muvarume.

Zviratidzo kana lymphoma iri muCentral Nervous System (CNS)

Zviratidzo zve lymphoma muCNS yako zvine hukama nemabasa ehuropi hwako, maziso uye musana. Izvo zvinoenderana nekuti ndeipi chikamu cheCNS chako chakakanganisika uye chinogona kusanganisira zvinotevera:

  • headaches
  • kuchinja kuchiono chako
  • kuvhiringidzika kana kushanduka kwendangariro
  • kuchinja kwekuziva (kuva nehope uye kusapindura)
  • kunetseka kutaura kana kumedza
  • kuchinja kwemaitiro ako kana hunhu hwako
  • kugumburwa (kukwana)
  • kushungurudza uye kurutsa
  • kurasikirwa kwechido (kusada kudya) uye kuora muviri
  • kunetsa kuenda kuchimbuzi
  • kunetseka kufamba, kusagadzikana kana kudonha
  • kushaya simba, chiveve kana kurira manzwiro.

Kuongororwa, kuiswa uye kugadzika kwePCNSL

Kana chiremba wako achifungidzira kuti unogona kuva ne lymphoma iwe uchada kuva nemiedzo yakawanda yakaitwa. Kusiyana nemamwe ma subtypes e-lymphoma, kurongedza hakuitike kana uine PCNSL nekuti lymphoma inongovharirwa kune yako central nervous system (CNS). Chero kupararira kunze kwe CNS kazhinji kunowanikwa muvarume chete uye kuma testes chete. 

PCNSL inogara ichionekwa seyepamusoro-grade lymphoma zvinoreva kuti ine hutsinye. Inokura nekukurumidza uye inogona kufamba kuburikidza neCNS yako nekukurumidza. Masero ane kenza anonzi B-cell (lymphoma cells) anotaridzikawo akasiyana zvakanyanya neako ane hutano B-cell nekuti anokura nekukurumidza uye haana nguva yekuumbwa zvakanaka.

Dzvanya pane musoro uri pazasi kuti udzidze zvakawanda nezve mhando yebvunzo dzaungango ongorora, uye dzidza zvakawanda nezve PCNSL yako.

Biopsy

Kuti uongorore PCNSL iwe uchada biopsy. A biopsy inzira yekubvisa chikamu, kana yese ye lymph node yakakanganisika kana nyama yakakanganisika. Munguva yekuitwa iwe unogona kunge uine general kana yemuno anesthetic kuti uwedzere kugadzikana, kana kuve nechokwadi kuti hauna kumuka pazvinenge zvichiitwa.

Mhando yebiopsy inofanira kuitwa inobva pane iyo lymphoma iripo.

Kana iyo lymphoma inofungidzirwa kuva mune yako:

  • Uropi - neurosurgeon (nyanzvi mukuongorora nekurapa matambudziko neCNS) inotora uropi biopsy. Mapundu (kana sampuli dzemapundu) mukati mehuropi hwako achabviswa uchishandisa CT scan kubatsira kutungamira tsono yebiopsy kunzvimbo chaiyo. Izvi zvinonzi a 'stereotactic biopsy'. Iwe uchave uine general anesthetic yeiyi maitiro sezvo zvakakosha kuti usafambe.
  • Ziso - an ophthalmologist (nyanzvi muzvirwere uye kukuvara kweziso) inogona kutora zvishoma zve vitreous (gel-sechinhu chiri mukati meziso rako) kutarisa lymphoma masero.
  • Muzongoza - nyanzvi yeradiologist inogona kutora biopsy kubva kumusana wako.

Kuyera ropa

Kuongororwa ropa kunotorwawo paunenge uchiedza kuongorora lymphoma yako, asiwo munguva yose yekurapa kuitira kuti chiremba awane kunzwisisa zviri nani nezvehutano hwako hwose, uye iva nechokwadi chokuti nhengo dzako dziri kushanda nemazvo kuti urarame nekurapa.

Iyi scan inowanzopa mifananidzo yakanakisa yehuropi hwako uye zvimwe zvikamu zveCNS uye inogona zvakare kuona musana wemuzongoza.

MRI
MRI scan yeuropi

Izvi zvinowanzoitwa kuti zvione lymphoma kune imwe nzvimbo mumuviri. Vanopa mifananidzo yakadzama inopa ruzivo rwakawanda kupfuura yakajairwa X-ray. Vanogonawo kuitwa kutarisa mapfupa ari musana wako.

CT scan

Mhando iyi yekuongorora inowanzoshandiswa pamwe chete neCT scan kuti ione lymphoma inoshanda kune imwe nzvimbo mumuviri wako. Zvinotora mufananidzo wemukati memuviri wako wese. Iwe uchapihwa tsono ine mumwe mushonga uyo masero egomarara senge lymphoma masero, anonwa. Mushonga unobatsira PET scan kuti ione kuti lymphoma iripi uye saizi uye chimiro nekusimbisa nzvimbo dzine lymphoma masero. Izvi dzimwe nguva zvinonzi "zvinopisa".  

Sezvo PCNSL inogona kukanganisa maziso iwe ungadawo bvunzo dzakasiyana dzemaziso. Chiremba wemaziso (nyanzvi yemaziso) achashandisa ophthalmoscope - chiridzwa chine chiedza uye chidiki chekukudza lens - kuti uwane kutarisa kwakanaka mukati meziso rako. Mamwe maedzo ekufungidzira anogona kuitwa uye aya anobatsira chiremba wemaziso kutarisa bundu pamwe nekuona kana gomarara rapararira.

 

A biopsy yeziso inogona kudiwa. Izvi zvinonzi vitrectomy. Karidzwa kadiki kanopinzwa muziso uye kanotora sampuli dzejelly-like vitreous, chinova chinhu chinozadza pakati peziso.

A testicular ultrasound yevarume bvunzo inowana mifananidzo yemachende nematishu akatenderedza muscrotum. Iyi ultrasound inogona kuitwa sezvo imwe PCNSL inogona kupararira kuma testes.

Results

Kumirira mhedzisiro yako yese kuti iuye inogona kuve nguva inoshungurudza iwe nevadikanwi vako. Zvakakosha kutaura pamusoro pemanzwiro auri kuita uye kubuda pachena kune avo vakakupoteredza pamusoro pezvaunoda. Vanhu vazhinji vanoda kubatsira, asi havazivi kuti sei saka nekuvazivisa zvaunoda, unogona kuvabatsira kupa rubatsiro rwaunoda.

Zvinogona kubatsirawo kutanga kuronga zvaungade mumwedzi iri kuuya kana uchida kurapwa. Isu takaisa mamwe matipi pamwechete pane yedu Kurarama neLymphoma - Iyo Inoshanda Stuff peji rewebhu. Dzvanya pane iyi link iripazasi kuti utungamirirwe kune iyo peji.

Unogona zvakare kubata Nharembozha yedu yeNurse kuti utaure nemumwe wedu Lymphoma Care Nurses. Ingobaya paBata nesu bhatani pazasi pepeji ino.

Iwe unogona zvakare kufarira kujoinha rimwe remapeji edu epasocial media kuti utaure nevamwe vanhu vanogara navo. Batanidza nemapeji edu esocial media nekudzvanya ma link ari pamusoro pepeji.

Kuti uwane rumwe ruzivo ona
Kurarama neLymphoma - The Practical Stuff

Kurapa kwePCNSL

Kuva neruzivo rwakakodzera kunogona kukubatsira kuti unzwe uine chivimbo uye kuziva zvekutarisira, uye kunogona kukubatsira kuronga pachine nguva pane zvaungade. Asi zvinogona kunetsa kuziva kuti ndeipi mibvunzo yekubvunza paunenge uchitanga kurapwa. Kana iwe usingazive, zvausingazive, ungaziva sei zvekubvunza?

Takaisa pamwechete rondedzero yemibvunzo yaungawana inobatsira. Zvechokwadi, mamiriro ezvinhu emunhu wose akasiyana, saka mibvunzo iyi haitauri zvose, asi inopa mavambo akanaka. Dzvanya pane chinongedzo chiri pazasi kuti uwane kopi yePDF yaunogona kudhawunirodha nekuprinda kana uchida.

Dzvanya pano kuti utore Mibvunzo yekubvunza chiremba wako usati watanga kurapwa.

Kuchengetedza mbereko

Kunyangwe iwe uri murume kana mukadzi, mazhinji ekurapa cancer anogona kukanganisa kubereka kwako - kugona kwako kugadzira vana. Kana iwe uchida kuva nevana mushure mekurapwa, kana usina chokwadi kana uchida, taura nachiremba wako pamusoro pezvipi zvingasarudzwa zvinogona kubatsira kuchengetedza kubereka kwako panguva yekurapa.

Mhedziso yemhando dzekurapa

Dzvanya kuburikidza nemasiraidhi ari pasi apa kuti uone nezvemhando dzakasiyana dzekurapa dzaungagone kupihwa kurapa PCNSL yako.

Steroid Treatment
Iwe unogona kunge wakatangwa pane steroid kana iwe waita mabiopsies ako aitwa. Steroids inobatsira kuderedza kuzvimba kwakatenderedza nzvimbo ye lymphoma uye inogona kubatsira kuvandudza zviratidzo zvako. Zvinowanzotangwa mushure mezvinyorwa nokuti lymphoma inogona kuva yakaoma kuongorora kana steroid yatopiwa.

Zvisinei, kana iwe uine zviratidzo zvakakomba uye chiremba wako ane chivimbo chokuti une PCNSL, vanogona kusarudza kutanga steroid kuti uvandudze zviratidzo zvako kunyange usati waita biopsy.

Steroids zvakare ine chepfu kune lymphoma masero saka vanogona kubatsira kuderedza lymphoma vachimirira kumwe kurapwa kutanga.

Steroids inogona kupihwa intravenously (kuburikidza netsinga) kana nemuromo (nemuromo). A common steroid is dexamethasone.
Chemotherapy (chemo)
Unogona kuva nemishonga iyi sepiritsi uye/kana kupihwa sekudonhedza (kupinza) mutsinga yako (muropa rako) kukiriniki yegomarara kana kuchipatara. Chemo inouraya maseru ari kukurumidza kukura saka inoshanda kurwisa aggressive lymphomas, asi inogona kukanganisa mamwe maseru ako akanaka anokura nekukurumidza, zvichikonzera zvisingadiwe mhedzisiro.

Chemo yaunowana yePCNSL inogona kunge yakasiyana nevanhu vane mamwe ma subtypes e lymphoma, sezvo mishonga inoda kuyambuka ropa-brain barrier yako kuti uende kune lymphoma yako. Zvakajairika kuve nechemotherapy ine immunotherapy senge rituximab.
Monoclonal antibody
Monoclonal antibodies dzimwe nguva anonzi immunotherapy nekuti anobatsira immune system yako kuziva uye kurwisa lymphoma.

Unogona kunge uine MAB infusion kukiriniki yegomarara kana kuchipatara. MABs inonamatira kune lymphoma cell uye inokwezva zvimwe zvirwere-kurwisa masero machena eropa uye mapuroteni kune kenza kuitira kuti immune system yako irwise PCNSL.
Kurapa kweRadiation
Radiotherapy inoshandisa mwaranzi kuuraya masero egomarara. Zvakafanana ne-high-energy X-rays uye inoitwa mazuva ese, kazhinji kubva Muvhuro kusvika Chishanu kwemavhiki akati wandei.

Hwose-brain radiotherapy inowanzo shandiswa semusanganiswa kurapwa mushure mechemotherapy.

Kusvikira pakati pemakore makumi mapfumbamwe ndiyo yaive yakanyanya kurapwa kwePCNSL, zvisinei ikozvino yakapihwa pamwe chete nechemotherapy. Mishonga yekubatanidza inotarisira kuderedza njodzi yekudzokazve (iyo lymphoma inodzoka). Radiotherapy inogona kushandiswa pachayo kana iwe usingakwanisi kushivirira chemotherapy.
Stem cell kuisirwa
Kana iwe uri mudiki uye uine aggressive lymphoma, SCT inogona kukurudzirwa sekurapa, kunyangwe kurapwa uku kusingakodzeri munhu wese.

A SCT inoitirwa kutsiva bhonzo rako rine chirwere nemasero matsva anogona kukura kuva masero matsva eropa ane hutano. NeSCT, stem masero anobviswa kubva muropa. Masero e stem anogona kubviswa kubva kune anopa kana kutorwa kubva kwauri mushure mekunge waita chemotherapy.

Kana stem masero achibva kune anopa, inonzi allogeneic stem cell transplant. Kana masero ako ega akaunganidzwa, anonzi autologous stem cell transplant.
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Mutsara wekutanga kurapwa

Unozofanirwa kutanga kurapwa mushure mekunge zvese zvawawana pakuongororwa zvadzoka. Mune zvimwe zviitiko, unogona kutanga zvese zviwanikwa zvebvunzo zvisati zvapinda. Zvinogona kuve zvakanyanya kana watanga kurapwa. Ungave uine mifungo yakawanda pamusoro pokuti uchararama sei, mabatiro aunoita kumba, kana kuti kurwara kwaungagona kurwara.

Ita kuti boka rako revarapi rizive kana uchifunga kuti ungangoda rubatsiro rwakawedzerwa. Vanogona kukubatsira nekukuendesa kunoona mushandi wezvekugarisana nevamwe kana imwe nyanzvi yezvehutano kuti ikubatsire kugadzirisa mamwe matambudziko emazuva ese aungasangana nawo. Unogonawo kusvika kune Lymphoma Care Nurses nekudzvanya pakanzi “Bata nesu” pazasi pepeji ino.

Kana watanga kurapwa kekutanga, kunonzi 'first-line treatment'. Unogona kuva nemishonga inodarika mumwechete, uye izvi zvinogona kusanganisira radiotherapy, chemotherapy kana monoclonal antibody.

Iyo yakajairwa mutsara wekutanga kurapwa inogona kusanganisira:

 High-dose methotrexate 

Izvi zvinogona kusanganiswa ne kana pasina monoclonal antibody, rituximab.

 MATRix

Uyu musanganiswa wemishonga yakasiyana yechemotherapy uye monoclonal antibody - methotrexate, cytarabine, thiotepa uye rituximab - yePCNSL ichangobva kuongororwa.

R-MPV (Chikamu chekutanga uye Chikamu chechipiri)

Chikamu chekutanga - Monoclonal antibody (rituximab) uye kusanganiswa kwechemotherapy kusanganisira methotrexate, procarbazine uye vincristine.

Chikamu chechipiri - High-dose chemotherapy - cytarabine

Methotrexate uye cytarabine

Musanganiswa wemachemotherapies maviri ePCNSL achangobva kuongororwa.

Intrathecal chemotherapy

Iyi ndiyo chemotherapy iyo inopiwa mumvura yemusana nenzira yekuputika kwechiuno. Izvi zvinoitwa kana lymphoma inowanikwa mumusana wako wemvura.

Clinical kuedza kubatanidzwa

Izvi zvinogona kusanganisira miedzo yekiriniki yekunangwa marapirwo uye mamwe marapirwo. Bvunza chiremba wako kana uchikodzera kune chero yekutanga-mutsara wekurapwa miedzo yekiriniki.

Radiotherapy kana Stem Cell Transplant

Kana iyo lymphoma ikadaira kuchemotherapy, timu yako yezvechiremba inogona kupa pfungwa-yakazara radiotherapy kana an autologous stem cell transplant (ona pamusoro). Aya ndiwo marapirwo ekubatanidza, zvinoreva kuti anoshandiswa kuderedza njodzi yekudzokera shure mushure mekubudirira kurapwa.

Chechipiri-mutsara uye inoenderera mberi kurapwa

Kana CNS lymphoma yako ikadzoka (inodzoka) kana kuti inoramba (isingapinduri) kurapwa, panogona kunge kune mamwe marapirwo aripo.

Kurapa kwauinako kana ukadzokera shure kana kuti PCNSL isingarambi kunonzi kurapwa kwechipiri. Mushonga wacho unoenderana nekuti wakakwana sei panguva iyoyo, kurapwa kwawakamboita uye kuti lymphoma iri kukukanganisa sei. Nyanzvi yako inogona kutaura newe kuburikidza nesarudzo dzako, dzingasanganisira:

  • Yakanyanya kusimba (yakasimba) chemotherapy, inogona kuteverwa ne autologous stem cell transplant (isina kukodzera kune vamwe vanhu).
  • Radiotherapy – kana isati yatopihwa.
  • Palliative marapirwo anopiwa nechinangwa chekudzikisa zviratidzo.
  • Clinical kuedza kubatanidzwa.

Clinical Trials

Zvinokurudzirwa kuti chero nguva yaunoda kutanga mishonga mitsva unobvunza chiremba wako nezvemakiriniki ekuedza iwe unogona kukodzera.

Miedzo yemakiriniki inzira yakakosha yekutsvaga mishonga mitsva, kana misanganiswa yemishonga yekuvandudza marapirwo ePCNSL mune ramangwana. Vanogona zvakare kukupa mukana wekuyedza mushonga mutsva, musanganiswa wemishonga kana kumwe marapirwo ausingakwanise kuwana kunze kwekuedzwa. Kana iwe uchida kutora chikamu muchirongwa chekiriniki, bvunza chiremba wako kuti ndeapi miedzo yekiriniki yaunokodzera. 

Kune marapirwo mazhinji uye misanganiswa yekurapa mitsva iri kuedzwa pari zvino mukuedzwa kwekiriniki kutenderera pasirese kune vanhu vane vese vachangobva kuongororwa uye vakadzokororwa / vanoramba PCNSL. Mamwe marapirwo ari kuongororwa ndeaya:

  • Ibrutinib (Imbruvica®)
  • Zanubrutinib (Brukinsa®) uye Tiselizumab
  • Pembrolizumab (Keytruda®)
  • GB5121 - Brain inopinda BTK inhibitor
Kuti uwane rumwe ruzivo ona
Migumisiro yekurapa

Kunzwisisa miedzo yekiriniki

Prognosis yePCNSL

Prognosis ishoko rinoshandiswa kutsanangura nzira ingangove yechirwere chako, kuti chichapindura sei kurapwa uye kuti uchaita sei panguva uye mushure mekurapwa.

Pane zvinhu zvakawanda zvinopa kufungidzira kwako uye hazvibviri kupa chirevo chakazara nezve prognosis.

Zvinhu zvinogona kukanganisa prognosis

 Zvimwe zvinhu zvinogona kukanganisa prognosis yako zvinosanganisira:

  • Zera rako uye hutano hwese panguva yekuongororwa
  • Mapinduriro aunoita pakurapwa

Dzimwe nguva zviratidzo zveCNS lymphoma zvinogadzirisa nekukurumidza nekurapa. Kutanga kurapwa nesteroids kunogona kubatsira zvakanyanya mukubvisa zviratidzo. Nekudaro, matishu etsinga anokura zvishoma nezvishoma, uye dzimwe nguva zvinogona kutora nguva kuti zviratidzo zviwedzere. Vamwe venyu vanogona kuona zvishoma nezvishoma kuvandudzwa kwezviratidzo, vamwe zvisinei, vanogona kuwana zviratidzo zvingasambogadzirisa zvizere, kunyanya kana vaivapo vasati varapwa.

Kuwana rutsigiro

Chikwata chako chekurapa chinogona kutsigira kupora kwako nekukuendesa kune vakakodzera nyanzvi. Kana iwe ukaona kushaya simba kwetsandanyama uye kurasikirwa kwesimba kana kusakurumidza kupora, iwe unofanirwa kufunga nezvekuona physiotherapist uye / kana occupational therapist sezvavanogona kupa rubatsiro nemazano ekuvandudza hupenyu hwehupenyu. Rubatsiro rwavo runogonawo kumisa zviratidzo kubva pakuipa kana mamwe matambudziko arikuitika mukufamba kwenguva.

Nyanzvi dzepfungwa dzinogona kupa tsigiro kana paine matambudziko ekuziva (kufunga) akadai sekurangarira kana kutarisisa matambudziko. Nyanzvi dzepfungwa uye vanachipangamazano vanogonawo kutsigira nemanzwiro eiyo lymphoma yako.

Zvakakosha kuziva kuti nzira dzekurapa dzePCNSL dzakavandudza zvikuru mumakore achangopfuura. Zvisinei, PCNSL inogona kuva yakaoma kurapa, uye mamwe marapirwo ane ngozi yekukonzera matambudziko ehutano kwenguva refu (matambudziko neuropi nemaziso). Matambudziko aya anowanda kana ukaonekwa uine CNS lymphoma kana wakura.  

 

Kupona - Kurarama, uye mushure megomarara

Mararamiro ane hutano, kana mamwe mararamiro akanaka anochinja mushure mekurapwa anogona kubatsira zvikuru kupora kwako. Pane zvinhu zvakawanda zvaunogona kuita kukubatsira kurarama zvakanaka mushure meBurkitt. 

Vanhu vazhinji vanoona kuti mushure mekuongororwa kenza, kana kurapwa, kuti zvinangwa zvavo uye zvavanokoshesa muhupenyu zvinoshanduka. Kusvika pakuziva kuti 'itsva yako yakajairika' chii kunogona kutora nguva uye kushungurudza. Zvinotarisirwa nemhuri yako neshamwari zvinogona kunge zvakasiyana nezvako. Iwe unogona kunzwa uri wega, wakaneta kana chero nhamba yemanzwiro akasiyana anogona kuchinja zuva rega rega.

Zvinangwa zvikuru mushure mekurapa lymphoma yako ndiko kudzokera kuhupenyu uye:            

  • shingairira sezvinobvira mubasa rako, mhuri, nemamwe mabasa ehupenyu
  • kuderedza migumisiro yechirwere uye zviratidzo zvegomarara uye kurapwa kwayo      
  • tsvaga uye gadzirisa chero mhedzisiro yekunonoka      
  • batsira kuti urambe wakasununguka sezvinobvira
  • vandudza hupenyu hwako uye chengetedza hutano hwakanaka hwepfungwa

Mhando dzakasiyana dzekugadzirisa kenza dzinogona kukurudzirwa kwauri. Izvi zvinogona kureva chero yemhando dzakasiyana zvemasevhisi akadai se:     

  • kurapa kwepanyama, kugadzirisa marwadzo      
  • kudya uye kuronga maekisesaizi      
  • manzwiro, basa uye mazano emari. 

pfupiso

  • Primary Central Nervous System Lymphoma (PCNSL) is a high-grade aggressive subtype yeNon-Hodgkin Lymphoma iyo inokura muhutano hwako hwepakati (CNS).
  • PCNSL haiwanzo kupararira kunze kweCNS asi inogona kupararira kuma testes muvarume.
  • PCNSL yakasiyana ne lymphomas inotanga kune imwe nzvimbo mumuviri uye inopararira kune CNS (secondary CNS lymphoma) uye inoda kurapwa zvakasiyana.
  • Zviratidzo zvePCNSL zvine hukama nenzvimbo ye lymphoma, kusanganisira zviratidzo zvine chekuita nemabasa ehuropi hwako, musana uye maziso.
  • Pane mhando dzakasiyana dzebvunzo dzauchazoda kuti uongorore PCNSL, uye izvi zvinogona kusanganisira maitiro apo iwe unopihwa general kana yemunharaunda anaesthetic.
  • Kurapa kwePCNSL kwakasiyana nemamwe ma subtypes e lymphoma sezvo mishonga inoda kupfuura nemuropa-brain barrier yako kuti uende kune lymphoma.
  • Zviratidzo zvinogona kutora nguva kuti zvive nani mushure mekurapa nekuda kwekukura zvishoma kwemasero etsinga, asi zvimwe zviratidzo zvinogona kukurumidza kukurumidza.
  • Taura nachiremba wako nezve mikana yako yekurapwa uye zvaunotarisira kubva mukurapwa kwako.
  • Hausi wega. Kana uchida kutaura nemumwe weVanamukoti vedu veLymphoma Care nezve lymphoma yako, marapirwo uye sarudzo tinya bhatani rekuti Taura nesu pazasi pescreen.

Tsigiro uye ruzivo

Dzidza zvakawanda pamusoro pekuongororwa ropa rako pano - Lab bvunzo online

Dzidza zvakawanda nezve marapirwo ako pano - eviQ anticancer kurapwa - Lymphoma

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