Ka Manaʻo o Anaplastic Large Cell Lymphoma (ALCL)
Anaplastic Large Cell Lymphoma (ALCL) he subtype kakaikahi a paʻakikī (wikiwiki) o PTCL. Hoʻokumu ʻo ALCL mai nā keʻokeʻo keʻokeʻo i kapa ʻia ʻo T-lymphocytes (T-cells) he ʻāpana o ko mākou ʻōnaehana pale, mālama iā mākou i ke olakino ma ke kaua ʻana i nā maʻi a me nā maʻi, a me ka hoʻoponopono ʻana i kā mākou mau pane pale.
ʻO nā subtypes o ALCL:
- ALCL pūnaewele - ALK +ve
- ALCL pūnaewele - ALK -ve
- Hoʻopili ʻia ka umauma pili (BIA)ALCL
- ʻO ka ʻili mua (Pc)ALCL
No ke aha i kapa ʻia ai ʻo Anaplastic Large Cell Lymphoma?
- ʻO ka Anaplastic ke ʻano o ka ʻokoʻa o nā cell mai nā T-cell olakino maʻamau.
- ʻO ke kelepona nui ʻo ia hoʻi ua ulu nui lākou ma mua o nā T-cell olakino.
- ʻO ka Lymphoma ke ʻano o ka maʻi kanesa o ke koko keʻokeʻo i kapa ʻia he lymphocytes.
I loko o ka ALCL, lilo kou mau lymphocytes T-cell i ka ma'i 'a'ai, e ulu nui ai, a 'oko'a loa mai kou mau kini T-ola. Hana ʻia kēia no ka mea ʻaʻole i hoʻonohonoho ʻia nā cell cancerous a ʻaʻole e ulu hou e like me ke ʻano o ka ulu ʻana. ʻO ka hopena, ʻaʻole hiki i nā pūnaʻi T lymphoma maʻi maʻi ke hana maikaʻi e pale iā ʻoe mai ka maʻi a me ka maʻi, a i ʻole e hoʻoponopono i kāu mau pane kūlohelohe.
Aia kekahi pūmua i loaʻa ma ka ʻili o ka cell ALCL i kapa ʻia ʻo 'CD30', e kōkua ana e hoʻokaʻawale i ka ALCL mai nā ʻano subtypes o PTCL. He mea nui e ʻike inā he CD30 maikaʻi kāu mau cell, no ka mea, ʻo kekahi lāʻau lapaʻau (Brentuximab vedotin) hiki ke hoʻohana ʻia no ka mālama ʻana i kekahi mau lymphoma e hana wale nō inā loaʻa kēia pūmua CD30 i kāu mau cell lymphoma.
He aha ke kumu o Anaplastic Large Cell Lymphoma (ALCL)?
E like me nā ʻano lymphoma he nui, ʻaʻole mākou ʻike i ke kumu e ulu ai ka ALCL i ka hapa nui o nā kānaka. Hoʻokahi ʻano subtype - BIA-ALCL wale nō i loaʻa i ka poʻe me nā implants umauma a ʻoi aku ka maʻamau i ka poʻe me nā implants silicone textured. Eia nō naʻe, he mea kakaikahi i waena o ka poʻe me nā implants, no laila ʻoiai ke hoʻonui nei nā implants i ka pilikia, ʻaʻole lākou e hoʻokumu i ka ALCL.
Nā moʻolelo maʻi e noho ana me, a i ʻole ma hope o ALCL
Ka hoʻomaopopo ʻana i nā Lymphocytes T-cell
Ka hoʻomaopopo ʻana i nā Lymphocytes T-cell
No ka hoʻomaopopo ʻana i ka ALCL, pono ʻoe e ʻike e pili ana i kāu lymphocytes T-cell.
He ʻāpana koʻikoʻi nā lymphocytes T-cell o kā mākou ʻōnaehana pale e pale iā mākou mai ka maʻi a me ka maʻi, a hoʻoponopono i kā mākou ʻōnaehana pale e pale aku i nā hōʻeha autoimmune. Hana ʻia ka hoʻouka kaua ʻana i ka wā ʻoi aku ka hana o kā mākou ʻōnaehana pale ʻole a hoʻomaka e hakakā i ko mākou kino ponoʻī ma mua o ka maʻi a me ka maʻi.
Hana ʻia nā pūnae T i loko o ko mākou iwi iwi, akā ma mua o ko lākou oʻo ʻana, hele lākou ma o kā mākou lymphatic system a hiki i ko mākou thymus kahi e hoʻomau ai lākou e ulu a oʻo.
E pili ana i nā Lymphocytes T-cell
- Hana ʻia nā pūnae T i loko o ko mākou iwi iwi, ʻoʻo i loko o ko mākou thymus, akā hiki ke noho ma kekahi ʻāpana o kā mākou lymphatic system - me kā mākou lymph nodes.
- Pono e ho'ā 'ia nā pūnaewele T e hana pono. Hoʻomaha maʻamau lākou i loko o kā mākou thymus, nā lymph nodes a i ʻole nā wahi ʻē aʻe o kāu ʻōnaehana lymphatic, a ala wale lākou a hakakā i ka maʻi i ka wā e hōʻike aku ai nā cell immune ʻē aʻe iā lākou he maʻi a maʻi paha e hakakā. I ko lākou ala ʻana, hiki i nā pūnae T ke hele i kekahi ʻāpana o ko mākou kino e hakakā i ka maʻi a i ʻole ka maʻi.
- ʻO kekahi mau T-cell ke kuleana no ka "hoʻoponopono" i ka pane immune. ʻO ia hoʻi, i ka wā i luku ʻia ai ka maʻi, ka “Nā pūnaewele T hoʻoponopono” e haʻi aku i nā pūnaewele ʻē aʻe e "kū i lalo" i ʻole lākou e hoʻomau i ka hakakā ʻana a hoʻopilikia i kā mākou mau sela maikaʻi ke pau ka maʻi.
- Ma hope o ka hakakā ʻana i kahi maʻi a i ʻole maʻi, lilo kekahi mau T-cell “Nā pūnāwai T hoʻomanaʻo” a hoʻomanaʻo lākou i nā mea a pau e ʻike ai e pili ana i ka maʻi a pehea e hakakā ai. ʻO ia ala, inā loaʻa hou iā mākou ka maʻi like a i ʻole ka maʻi, hiki i kā mākou ʻōnaehana pale ʻana ke hakakā me ka wikiwiki a me ka maikaʻi.
- Hiki i kekahi mau T-cell ke kōkua i nā mea ʻē aʻe, e like me nā lymphocytes B-cell e hana pono. Ua kapa ʻia kēia mau T-cell "Kōkua T-cell”.
Nā hōʻailona o ALCL
ʻOkoʻa nā hōʻailona o ALCL ma muli o ke ʻano subtype o ALCL iā ʻoe, a me nā ʻāpana o kou kino i loaʻa ka lymphoma i loko. ʻOkoʻa loa nā hōʻailona e loaʻa iā ʻoe mai kahi mea ʻē aʻe me ALCL.
Aia kekahi mau hōʻailona o ka lymphoma maʻamau i waena o nā poʻe he nui me ka lymphoma me ka ʻole o ke ʻano subtype. Hōʻike ʻia kēia mau hōʻailona maʻamau ma lalo nei.
Nā hōʻailona maʻamau o ka lymphoma
kekahi nā hōʻailona He mea maʻamau ia i nā ʻano lymphoma āpau no laila e loaʻa iā ʻoe kekahi o kēia mau hōʻailona:
ʻO nā puʻupuʻu lymph pehu e like me ka puʻupuʻu ma lalo o kou ʻili. Loaʻa pinepine ʻia kēia mau mea ma kou ʻāʻī, nā ʻāʻī a i ʻole ka ʻāʻī, no ka mea, ʻoi aku ka pili o kēia mau lymph nodes i kou ʻili ma mua o nā ʻāpana lymph ʻē aʻe. Eia nō naʻe, hiki ke hoʻopili ʻia kekahi lymph node, akā hiki ke loaʻa i ka wā CT a i ʻole nā scan ʻē aʻe.
Ka luhi - ʻaʻole i hoʻomaikaʻi ʻia ka luhi ma ka hoʻomaha a i ʻole ka hiamoe.
Pau ka ʻai - ʻaʻole makemake e ʻai.
ʻIli ʻili.
Pokole o ka hanu.
ʻEha ma kou ʻōpū a ʻōpū paha.
ʻOi aku ke koko a ʻeha paha ma mua o ka maʻamau.
B-hōʻailona.
Hoʻopili ʻia nā hōʻailona kikoʻī i kāu subtype o ALCL ma lalo o ka pauku ka nānā ʻana o nā subtype ALCL.
Pehea e ʻike ʻia ai ʻo Anaplastic Large Cell Lymphoma?
Inā manaʻo kāu kauka e loaʻa iā ʻoe ka lymphoma, pono lākou e hoʻonohonoho i nā hoʻokolohua koʻikoʻi. Pono kēia mau ho'āʻo e hōʻoia a hoʻopau paha i ka lymphoma ke kumu o kāu mau hōʻailona.
ke koko ho'āʻo ai i
Lawe ʻia nā hoʻāʻo koko i ka wā e hoʻāʻo ai e hōʻoia i kāu lymphoma, akā i loko o kāu mālama ʻana e hōʻoia i ka hana pono ʻana o kāu mau kino, a hiki ke hoʻokō i ka mālama ʻana.
Nā Biopsies
No ka ʻike ʻana i ka ALCL pono ʻoe i kahi biopsy. ʻO ka biopsy kahi hana e wehe ai i kahi ʻāpana, a i ʻole nā poʻo lymph i hoʻopilikia ʻia a/ a i ʻole kahi laʻana o ka iwi iwi. A laila nānā ʻia ka biopsy e nā ʻepekema i loko o kahi keʻena hana e ʻike inā he mau loli e kōkua i ke kauka e hōʻoia i ka ALCL.
Ke loaʻa iā ʻoe kahi biopsy, loaʻa paha iā ʻoe kahi maʻi anesthetic kūloko a i ʻole maʻamau. E pili ana kēia i ke ʻano o ka biopsy a me kahi ʻāpana o kou kino i lawe ʻia mai. Aia nā ʻano biopsies like ʻole, a pono paha ʻoe ma mua o hoʻokahi no ka loaʻa ʻana o ka laʻana maikaʻi loa.
Biopsy kumu a i ʻole ka nila maikaʻi
Lawe ʻia nā biopsies koʻikoʻi a i ʻole ka nila maikaʻi no ka wehe ʻana i kahi laʻana o ka puʻupuʻu lymph pehu a i ʻole ka ʻōpū e nānā i nā hōʻailona o GZL.
Hoʻohana maʻamau kāu kauka i kahi anesthetic kūloko e hoʻopau i ka wahi i ʻole ʻoe e ʻeha i ka wā o ke kaʻina hana, akā e ala ʻoe i kēia biopsy. A laila e hoʻokomo lākou i kahi nila i loko o ka ʻōpū lymph pehu a i ʻole ka puʻupuʻu a wehe i kahi laʻana o ka ʻiʻo.
Inā hohonu i loko o kou kino ka pehu lymph node a puʻupuʻu paha, hiki ke hana ʻia ka biopsy me ke kōkua o ke ultrasound a i ʻole ke alakaʻi x-ray (kiʻi).
Loaʻa paha iā ʻoe kahi maʻi anesthetic maʻamau no kēia (kahi e hiamoe ai ʻoe no kahi manawa liʻiliʻi). Loaʻa paha iā ʻoe kekahi mau humuhumu ma hope.
ʻOi aku ka nui o nā biopsies o ka nila ma mua o ka biopsy nila maikaʻi, no laila, ʻoi aku ka maikaʻi o ka koho i ka wā e hoʻāʻo ai e ʻike i ka lymphoma.
Nānā nui o nā ʻano subtype ALCL
Mai kāu biopsies, a ma ka nānā ʻana i kahi o kou kino i hoʻomaka ai ka lymphoma, hiki i kāu kauka ke hoʻoholo i ke ʻano subtype o ALCL iā ʻoe. He mea nui ka subtype e ʻike, no ka mea, hāʻawi ia i ka ʻike e pili ana i ke ʻano o nā lapaʻau e kūpono loa iā ʻoe. Inā ʻaʻole ʻoe i ʻike, e nīnau i kāu kauka he aha ka subtype o ALCL iā ʻoe, a pehea ka hopena o kēia i kāu lapaʻau.
ʻO ka ALCL ʻili mua he lymphoma molowa (ke ulu mālie) e hoʻomaka ana i loko o nā pūnaʻi T ma nā papa o kou ʻili. ʻAʻole like me nā ʻano subtype ʻē aʻe o ALCL, ʻaʻole pono ʻoe i kahi lapaʻau no PcALCL. E like me ka nui o nā ʻano lymphoma palaualelo, hiki iā ʻoe ke noho me PcALCL i ke koena o kou ola, akā he mea nui e ʻike, hiki iā ʻoe ke ola maikaʻi me ia, a ʻaʻohe hopena maikaʻi ʻole i kou olakino. Hoʻopilikia wale ia i kou ʻili a ʻokoʻaʻole laha ma mua o kou ʻili i nā wahi ʻē aʻe o kou kino.
Hoʻomaka maʻamau me ka ʻūhū a i ʻole nā puʻupuʻu ma kou ʻili e ʻeha a ʻeha paha, akā ʻaʻole paha e hōʻeha iā ʻoe. I kekahi manawa, ua like paha ia me ka ʻeha ʻaʻole hoʻōla e like me kou manaʻo. ʻO kēlā me kēia lāʻau lapaʻau o PcALCL he mea ia e hoʻomaikaʻi ai i ka ʻeha a i ʻole ka ʻeha, a i ʻole e hoʻomaikaʻi i ke ʻano o ka lymphoma ma mua o ka mālama ʻana i ka lymphoma ponoʻī. Eia naʻe, inā pili ka PcALCL i kahi ʻāpana liʻiliʻi loa o ka ʻili, hiki ke wehe ʻia me ka ʻoki ʻana a i ʻole ma o ka radiotherapy.
He mea maʻamau ka PcALCL i nā poʻe ma waena o 50-60 mau makahiki, akā hiki ke hoʻopilikia i kēlā me kēia makahiki, me nā keiki.
ʻO ALK +ve ALCL ka subtype maʻamau o ALCL. He lymphoma koʻikoʻi (wikiwiki) hiki ke hoʻomaka a laha i kekahi ʻāpana o kou kino, ʻo ia ke kumu i kapa ʻia ai ʻo systemic. I loko o ka ALK-positive ALCL, loaʻa ka hoʻololi genetic (mutation) o nā pūnaʻi T ʻinoʻino e hana ai i kahi protein i kapa ʻia ʻo 'anaplastic lymphoma kinase' (ALK). No ka mea, hana lākou i kēia pūmua, ua kapa ʻia ʻo ALK maikaʻi.
ʻOi aku ka maʻamau o ka ALK +ve ALCL i nā keiki a me nā ʻōpio ma lalo o 40 mau makahiki, ʻoiai hiki ke hoʻopilikia i kēlā me kēia makahiki. Hoʻopilikia ia i nā kāne ʻekolu mau manawa ma mua o nā wahine.
Inā loaʻa iā ʻoe ka ALK + ve ALCL hiki iā ʻoe ke loaʻa kekahi o nā hōʻailona i helu ʻia ma luna. Pili paha nā hōʻailona ʻē aʻe i kahi o kāu lymphoma. No ka laʻana, inā aia ka ALCL i loko o kou ʻōpū, loaʻa paha iā ʻoe ka ʻeha o ka ʻōpū a i ʻole ka hoʻololi ʻana i ke ʻano o ka hana ʻana o kou ʻōpū, a i ʻole ke koko i loko o kou ʻōpū (poo).
Pili ka ALK -ve ALCL ma kahi o 3 o kēlā me kēia 10 poʻe me ALCL. Kapa ʻia ʻo ia ʻo ALK -ve no ka mea ʻaʻole like me ALK + ve ALCL, ʻaʻole hana nā pūnaewele lymphoma i ka protein 'anaplastic lymphoma kinase' (ALK). Eia nō naʻe, e like me ALK + ve ALCL, he ʻano ʻano hoʻomāinoino (wikiwiki) hiki ke hoʻomaka a laha i kekahi ʻāpana o kou kino, ʻo ia ke kumu i kapa ʻia ai ʻo systemic.
He mea maʻamau ka ALK -ve ALCL i nā poʻe mākua waena ma kahi o 40-65 mau makahiki, akā hiki ke hoʻopilikia i nā kānaka o kēlā me kēia makahiki.
Inā loaʻa iā ʻoe ka ALK -ve ALCL hiki iā ʻoe ke loaʻa kekahi o nā hōʻailona i helu ʻia ma luna. Pili paha nā hōʻailona ʻē aʻe i kahi o kāu lymphoma.
Kapa ʻia ka Breast Implant Associated ALCL no ka mea, pili wale ia i ka poʻe me nā implants umauma. Ua ʻike ʻia ia i nā makahiki i hala iho nei, no laila ke aʻo ʻia nei nā mea hou aʻe e pili ana iā ia, akā ʻoi aku ka maʻamau inā ua hoʻopili ʻoe i nā implants silicone. Hoʻomaka ia ma ka umauma me ka implant a maʻamau ka ulu lohi (ʻoluʻolu) a loaʻa pinepine wale i ka umauma. Eia naʻe, ʻaʻole hiki ke hana ʻino a palahalaha ma waho o ka umauma.
ʻOiai ka hoʻomaka ʻana i ka umauma me ka implant, ʻaʻole ʻo BIA-ALCL kahi ʻano o ka maʻi kanesa o ka umauma, he lymphoma ia e hoʻomaka i ka wā e lilo ai nā lymphocytes T-cell i loko o ka umauma (ʻaʻole nā pūnaewele umauma). Ua manaʻo ʻia e ulu ana ma muli o ka ʻāʻā lōʻihi a puni ka umauma implant.
ʻAʻohe ou hōʻailona me BIA-ALCL a hiki ke ʻike ʻia inā loaʻa iā ʻoe kahi ultrasound a i ʻole mammogram. Inā loaʻa iā ʻoe nā hōʻailona i ka wā mua o ka BIA-ALCL, ʻike paha ʻoe i kahi puʻupuʻu a pehu paha ma kou umauma a puni ka implant. I loko o ka maʻi hope, loaʻa paha iā ʻoe kekahi o nā hōʻailona i helu ʻia ma luna.
ʻO ke kau ʻana o ka lymphoma
Ke ʻike ʻoe ua loaʻa iā ʻoe ka Anaplastic Large Cell Lymphoma, makemake kāu kauka e hana hou i nā hoʻokolohua e ʻike inā ua laha ka lymphoma i nā wahi ʻē aʻe o kou kino. Kapa ʻia kēia mau hoʻokolohua he staging.
E nānā nā ho'āʻo ʻē aʻe i ka ʻokoʻa o kāu mau cell lymphoma mai kāu mau T-cell maʻamau a me ka wikiwiki o ka ulu ʻana. Kapa ʻia kēia ka mākaʻikaʻi.
Kaomi ma nā poʻomanaʻo ma lalo no ka ʻike hou aku.
ʻO ka staging e pili ana i ka nui o kou kino i hoʻopilikia ʻia e kāu lymphoma a i ʻole, pehea ka lōʻihi o ka laha ʻana mai kahi i hoʻomaka mua ai.
Hiki i nā pūnae T ke hele i kekahi wahi o kou kino. 'O ia ho'i, hiki i nā pūnaewele lymphoma (nā T-cell ma'i 'a'ai), hiki ke hele i kekahi wahi o kou kino. Pono ʻoe e hoʻāʻo hou aʻe e ʻike i kēia ʻike. Kapa ʻia kēia mau hoʻokolohua he staging tests a ke loaʻa iā ʻoe nā hopena, e ʻike ʻoe inā loaʻa iā ʻoe ka pae mua (I), pae ʻelua (II), pae ʻekolu (III) a i ʻole ka pae ʻehā (IV) ALCL.
E pili ana kāu pae o ALCL i:
- ʻEhia mau wahi o kou kino i loaʻa i ka lymphoma.
- Aia ma kahi o ka lymphoma inā aia ma luna, ma lalo a ma nā ʻaoʻao ʻelua o kāu diaphragm (he ʻiʻo nui me ke ʻano dome ma lalo o kou iwi iwi ʻaoʻao e hoʻokaʻawale ana i kou umauma mai kou ʻōpū).
- Inā ua laha ka lymphoma i kou iwi iwi a i ʻole nā ʻano ʻē aʻe e like me ke ake, ka māmā, ka ʻili a i ʻole ka iwi.
Kapa ʻia nā pae I a me II 'o ka pae mua a i ʻole ka palena palena' (e pili ana i kahi ʻāpana o kou kino).
Ua kapa ʻia nā pae III a me IV he 'pae holomua' (ʻoi aku ka laulā).
Hana 1 | Hoʻopili ʻia kahi ʻāpana lymph node, ma luna a ma lalo paha o ka diaphragm |
Hana 2 | ʻelua a ʻoi aʻe paha nā wahi lymph node ma ka ʻaoʻao like o ka diaphragm |
Hana 3 | ma ka liʻiliʻi hoʻokahi wahi lymph node ma luna a ma ka liʻiliʻi hoʻokahi wahi lymph node ma lalo o ka diaphragm e hoʻopilikia ʻia |
Hana 4 | Aia ka lymphoma i loko o nā pūnana lymph he nui a ua laha i nā wahi ʻē aʻe o ke kino (e laʻa me ka iwi, ka māmā, ka ate) |
ʻO ka ʻike hoʻokūkū keu
Hiki i kāu kauka ke kamaʻilio e pili ana i kāu pae ma ka hoʻohana ʻana i kahi leka, e like me A,B, E, X a i ʻole S. Hāʻawi kēia mau leka i ka ʻike hou aku e pili ana i nā hōʻailona āu i loaʻa ai a i ʻole ka hopena o kou kino e ka lymphoma. Kōkua kēia ʻike a pau i kāu kauka e ʻimi i ka hoʻolālā lapaʻau maikaʻi loa no ʻoe.
palapala | Meaning | nui |
A a i ʻole B |
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E & X |
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S |
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(ʻO kou spleen he ʻōkana i loko o kāu ʻōnaehana lymphatic e kānana a hoʻomaʻemaʻe i kou koko, a he wahi ia e hoʻomaha ai kou mau cell B a hana i nā antibodies) |
Nā hoʻāʻo no ke kahua
No ka ʻike ʻana i ka pae āu e loaʻa ai, e noi ʻia paha ʻoe e loaʻa i kekahi o kēia mau hoʻokolohua staging:
Ka pākuʻina o ka tomography (CT)
Lawe kēia mau kiʻi i nā kiʻi o loko o kou umauma, ka ʻōpū a i ʻole ke pelvis. Hāʻawi lākou i nā kiʻi kikoʻī e hāʻawi i ka ʻike hou aku ma mua o kahi X-ray maʻamau.
ʻO ka ʻōmole helu Positron emoate (PET)
He scan kēia e kiʻi i nā kiʻi o loko o kou kino holoʻokoʻa. E hāʻawi ʻia ʻoe i kahi lāʻau lapaʻau e hoʻopaʻa ʻia ai nā cell cancerous - e like me nā cell lymphoma. ʻO ka lāʻau lapaʻau e kōkua ana i ka PET scan e ʻike i kahi o ka lymphoma a me ka nui a me ke ʻano ma ke kuhikuhi ʻana i nā wahi me nā cell lymphoma. Ua kapa ʻia kēia mau wahi he "wela".
Pahu lumbar
ʻO ka ʻoki ʻana i ka lumbar kahi hana i hana ʻia e nānā inā ua laha ka lymphoma iā ʻoe ʻōnaehana ʻōnaehana waena (CNS), e pili ana i kou lolo, spinal cord a me kahi wahi a puni kou mau maka. Pono ʻoe e noho mālie i ka wā o ke kaʻina hana, no laila e loaʻa i nā pēpē a me nā keiki kahi maʻi maʻi maʻamau e hoʻomoe iā lākou i ka wā e hana ʻia ai ke kaʻina hana. Pono ka hapa nui o ka poʻe mākua i kahi anesthetic kūloko no ke kaʻina hana e hoʻopau ai i ka wahi.
Na kāu kauka e hoʻokomo i ka nila ma kou kua, a e lawe i kahi wai liʻiliʻi i kapa ʻia ʻo "ka wai o ke kuamoʻo o ka lolo” (CSF) mai a puni kou iwi kuamoʻo. ʻO ka CSF kahi wai e hana like me ka mea hoʻopuʻi i kou CNS. Lawe pū ia i nā protein like ʻole a me nā maʻi e hakakā ana i nā cell immune e like me nā lymphocytes e pale i kou lolo a me ke kuamoʻo. Hiki nō hoʻi iā CSF ke kōkua i ka hoʻokahe ʻana i kekahi wai ʻē aʻe i loaʻa iā ʻoe i loko o kou lolo a i ʻole a puni kou iwi kuamoʻo e pale ai i ka pehu ʻana ma ia mau wahi.
A laila e hoʻouna ʻia ka laʻana CSF i ka pathology a nānā ʻia no nā hōʻailona o ka lymphoma.
Biopsy iwi ʻōiwi
- ʻO ka aspirate iwi iwi (BMA): lawe ʻia kēia hoʻāʻo ʻana i kahi wahi liʻiliʻi o ka wai i loaʻa ma ka hakahaka o ka iwi.
- ʻO ka iwi aspirate trepine (BMAT): lawe kēia ho'āʻo i kahi laʻana liʻiliʻi o ka ʻiʻo iwi iwi.
Hoʻouna ʻia nā laʻana i ka pathology kahi e nānā ʻia ai nā hōʻailona o ka lymphoma.
Hiki ke ʻokoʻa ke kaʻina hana no nā biopsies iwi iwi ma muli o kahi āu e mālama ai, akā e hoʻokomo pinepine ʻia kahi anesthetic kūloko e hoʻopau i ka wahi.
Ma kekahi mau haukapila, hiki ke hāʻawi ʻia iā ʻoe i ka hoʻomaha māmā e kōkua iā ʻoe e hoʻomaha a hiki ke kāpae iā ʻoe mai ka hoʻomanaʻo ʻana i ke kaʻina hana. ʻAʻole pono ka nui o ka poʻe i kēia a loaʻa paha i kahi "whistle green" e omo ai. He lāʻau hōʻeha ʻeha ko loko o kēia puʻupuʻu ʻōmaʻomaʻo (i kapa ʻia ʻo Penthrox a i ʻole methoxyflurane), āu e hoʻohana ai e like me ka mea e pono ai i ke kaʻina hana.
E hōʻoia ʻoe e nīnau i kāu kauka i nā mea i loaʻa e hōʻoluʻolu iā ʻoe i ka wā o ke kaʻina hana, a e kamaʻilio pū me lākou e pili ana i kou manaʻo he koho maikaʻi loa ia no ʻoe.
Hiki ke loaʻa ka ʻike hou aku e pili ana i nā biopsies iwi ma kā mākou ʻaoʻao pūnaewele ma aneʻi
He ʻokoʻa ka ulu ʻana o kāu mau sela lymphoma, a ʻokoʻa ka nānā ʻana i nā cell maʻamau. ʻO ka pae o kāu lymphoma ka wikiwiki o ka ulu ʻana o kāu mau sela lymphoma, e pili ana i ka nānā ʻana ma lalo o kahi microscope. ʻO nā papa he 1-4 (haʻahaʻa, waena, kiʻekiʻe). Inā loaʻa iā ʻoe kahi lymphoma papa kiʻekiʻe, ʻokoʻa loa ke ʻano o kāu mau pūnaewele lymphoma mai nā pūnaewele maʻamau, no ka mea ke ulu wikiwiki nei lākou e ulu pono. Aia ma lalo kahi ʻike o nā māka.
- G1 - papa haʻahaʻa - ke nānā aku nei kāu mau cell i kahi maʻamau, a ulu lākou a pālahalaha mālie.
- G2 – papa waena – ke hoʻomaka nei kāu mau cell e nānā ʻokoʻa akā aia kekahi mau cell maʻamau, a ulu a laha lākou ma kahi wikiwiki.
- G3 – papa kiʻekiʻe – ʻokoʻa ke ʻano o kāu mau cell me kekahi mau cell maʻamau, a ulu lākou a pālahalaha wikiwiki.
- G4 - papa kiʻekiʻe - ʻokoʻa loa kāu mau cell i ka mea maʻamau, a ulu a palahalaha loa lākou.
Hoʻohui kēia ʻike āpau i ke kiʻi holoʻokoʻa a kāu kauka i kūkulu ai e kōkua i ka hoʻoholo ʻana i ke ʻano o ka lāʻau lapaʻau maikaʻi loa no ʻoe.
He mea nui e kamaʻilio me kāu kauka e pili ana i kāu mau mea pilikia ponoʻī i hiki iā ʻoe ke ʻike maopopo i ka mea e manaʻo ai mai kāu mau lapaʻau.
Ke kali nei i nā hualoaʻa
ʻO ke kali ʻana i kāu hopena he manawa kaumaha a hopohopo. He mea nui e kamaʻilio e pili ana i kou manaʻo. Inā he hoaaloha hilinaʻi a ʻohana paha kāu hiki ke kamaʻilio me lākou. Akā, inā ʻaʻole ʻoe manaʻo hiki iā ʻoe ke kamaʻilio me kekahi i kou ola pilikino, e kamaʻilio me kāu kauka kūloko, hiki iā lākou ke kōkua i ka hoʻonohonoho ʻana i ka ʻōlelo aʻoaʻo a i ʻole ke kākoʻo ʻē aʻe no laila ʻaʻole ʻoe hoʻokahi i kou hele ʻana i nā manawa kali a me ka mālama ʻana no ALCL.
Hiki iā ʻoe ke hoʻokaʻaʻike i kā mākou Lymphoma Care Nurses ma ke kaomi ʻana i ke pihi Hoʻokaʻaʻike iā mākou ma lalo o ka pale. A i ʻole inā aia ʻoe ma Facebook a makemake e hoʻopili i nā maʻi ʻē aʻe e noho ana me ka lymphoma hiki iā ʻoe ke hui pū me mākou Lymphoma i lalo palapala.
Ma mua o kou hoʻomaka ʻana i ka lāʻau lapaʻau
Hiki ke laha koke nā ʻano subtypes o ALCL, no laila pono ʻoe e hoʻomaka i ka lapaʻau ma hope koke o kou ʻike ʻia ʻana. Eia nō naʻe, aia kekahi mau mea e noʻonoʻo ai ma mua o kou hoʻomaka ʻana i ka mālama ʻana.
Māmā
Hiki i kekahi mau lāʻau lapaʻau no ka lymphoma ke hoʻopilikia i kou ulu ʻana, e paʻakikī ai ka hāpai ʻana, a i ʻole ka hāpai ʻana i kekahi. Hiki i kēia ke hana me kekahi mau ʻano lāʻau anticancer e like me:
- chemotherapy
- radiotherapy (inā he nui kou pelvis)
- nā lāʻau lapaʻau antibody (monoclonal antibodies a me nā mea hoʻopaʻa hoʻopaʻa pale pale)
- ka hoʻololi ʻana i ke kelepona (no ka chemotherapy nui e pono ai ʻoe ma mua o ka hoʻololi ʻana).
Nā nīnau e nīnau i kāu Kauka
Lapaʻau ʻana o ALCL
Ke hoʻopau ʻia nā hopena a pau mai kāu biopsy a me ka staging scans, e nānā kāu kauka iā lākou e hoʻoholo i nā koho lapaʻau maikaʻi loa no ʻoe. Hiki paha iā lākou ke hui pū me nā loea ʻē aʻe i kahi hālāwai multidisciplinary e hōʻoia i ka uhi ʻia o kāu mau pono āpau.
ʻO kekahi mau mea a lākou e noʻonoʻo ai i ka wā e hoʻoholo ai i nā koho lapaʻau maikaʻi loa e hāʻawi iā ʻoe:
- ka subtype a me ka pae o lymphoma i loaʻa iā ʻoe
- nā hōʻailona āu e loaʻa nei
- pehea ka hopena o ka lymphoma i kou kino
- kou makahiki
- nā maʻi maʻi ʻē aʻe āu e loaʻa ai, nā lāʻau lapaʻau āu e lawe nei, a me kou olakino a maikaʻi
- kou mau makemake pono'ī ke loaʻa iā ʻoe ka ʻike āpau.
Ma mua o ka hoʻomaka ʻana o ka mālama ʻana, pono e hāʻawi ʻia ka ʻike kūpono e pili ana i ka lāʻau i hoʻolālā ʻia, nā hopena ʻaoʻao a me nā mea e kali ai. ʻO ka hoʻonaʻauao ʻana mai nā kahu maʻi maʻi maʻi ma mua o ka loaʻa ʻana o ka lāʻau lapaʻau, hiki ke kōkua nui a pono e hoʻokomo i nā ʻōlelo aʻoaʻo e pili ana i ka maʻi ʻole a i ʻole ke kōkua ʻana i ke kauka a kahu hānai paha.
Inā paʻa kāu PcALCL i kou ʻili, ʻaʻole e hōʻeha iā ʻoe i nā hōʻailona a i ʻole pilikia, ʻaʻole pono ʻoe i kahi lapaʻau. ʻO kēia no ka mea ʻo PcALCL i paʻa i kou ʻili ʻaʻole ia e pōʻino i kou olakino a ʻaʻole ia e hoʻopōkole i kou ola.
Inā hōʻeha kāu PcALCL i ka ʻeha, ka ʻuʻu a i ʻole ke kahe ʻana o ke koko a i ʻole ke ʻano o ia mea e hoʻopilikia ai iā ʻoe, hiki iā ʻoe ke loaʻa ka lāʻau lapaʻau e hoʻomaikaʻi ai i kēia mau hōʻailona. ʻAʻole ka lāʻau lapaʻau e hoʻōla iā ʻoe i ka PcALCL, akā no ka mālama ʻana i nā hōʻailona.
Lapaʻau no ka pae mua o PcALCL
Nā lāʻau lapaʻau - nā ʻaila a i ʻole nā lotion āu e holo ai i kahi o ka ʻili i hoʻopilikia ʻia.
ʻO nā steroid intralesional – Hiki ke hoʻohana ʻia ia mau mea inā ʻaʻole pono nā lāʻau lapaʻau. Na kāu kauka e hoʻokomo i kahi mea steroid i loko o kahi o kou ʻili i hoʻopilikia ʻia e ka PcALCL. He mea ʻawaʻawa nā steroids i nā pūnaewele lymphoma, no laila hiki ke hōʻemi i ka nui o nā pūnaewele lymphoma ma ia wahi a hoʻomaikaʻi i kāu mau hōʻailona.
ʻO ke kelepona - Hiki ke hāʻawi ʻia iā ʻoe ka radiotherapy, ʻo ia ka lāʻau lapaʻau e hoʻohana ana i ka radiation e like me ka X-ray, proton beams a i ʻole nā kukui gamma e hoʻopau i nā cell lymphoma.
Ho'āla – Hiki paha i kāu PcALCL ke wehe loa me ka ʻoki. E pili ana kēia i ka nui a me ka wahi o kāu PcALCL.
Lapaʻau no ka pae holomua PcALCL
Hiki i ka BIA-ALCL ke molowa a pili i kou umauma, a i ʻole e ʻoi aku ka huhū a hoʻolaha i nā wahi ʻē aʻe o kou kino e pili ana i kāu mau lymph nodes a me nā ʻōpū.
ʻO ka hoʻolālā lapaʻau e hāʻawi ʻia e kāu kauka, e hoʻohālikelike ʻia i ke ʻano o kāu BIA-ALCL a me ka lōʻihi o ka laha ʻana.
BIA-ALCL mua
No ka BIA-ALCL mua loa i loko o kou umauma wale nō, pono ʻoe e ʻoki wale i ka implant a me nā wahi i loaʻa i ka lymphoma i loko o ka umauma. Hiki paha iā ʻoe ke hoʻokomo i nā implants ʻokoʻa ma hope o ke ʻoki ʻana a i ʻole e hoʻoholo paha ʻaʻole. He kamaʻilio kēia me kāu kauka lapaʻau a me ka hematologist e kōkua iā ʻoe e hoʻomaopopo i nā pilikia a me nā pono o nā implants like ʻole.
Nui nā kumu i loaʻa ai i nā kānaka nā implants o ka umauma, a ʻo ka manaʻo o ka wehe ʻana iā lākou, a me ka loaʻa ʻana o kahi hōʻailona lymphoma hiki ke lilo i mea kaumaha loa. Inā ʻoe e hakakā nei me kou mau manaʻo i kēia manawa, e ʻoluʻolu e kelepona i kāu hui lapaʻau. Loaʻa ke kōkua e hoʻokō iā ʻoe, a kōkua iā ʻoe e hana i nā hoʻoholo maikaʻi e pili ana i kou olakino.
BIA-ALCL hope loa
BvCHP - cyclophosphamide, doxorubicin, prednisolone a me kahi antibody monoclonal i kapa ʻia ʻo brentuximab vedotin (Bv). Hoʻohana wale ʻo Bv i nā lymphomas me kahi pūmua i kapa ʻia ʻo CD30 ma luna o lākou.
kua - ka chemotherapy hui pū o cyclophosphamide, doxorubicin, vincristine a me kahi steroid i kapa ʻia he prednisolone.
CHOEP - like me CHOP akā me kahi chemotherapy hou i kapa ʻia ʻo etoposide.
ʻO ALK +ve ALCL pūnaewele kahi ʻano lymphoma maʻamau a paʻakikī no laila pono ʻoe e hoʻomaka i ka lapaʻau ma hope koke o kou ʻike ʻia ʻana. Hiki ke mālama ʻia ka chemotherapy me ka radiotherapy a i ʻole.
- ʻO Chemotherapy - ʻO nā protocols chemotherapy maʻamau i hoʻohana ʻia no ka ALCL systemic:
BvCHP - cyclophosphamide, doxorubicin, prednisolone a me kahi antibody monoclonal i kapa ʻia ʻo brentuximab vedotin (Bv). Hoʻohana wale ʻo Bv i nā lymphomas me kahi pūmua i kapa ʻia ʻo CD30 ma luna o lākou.
kua - ka chemotherapy hui pū o cyclophosphamide, doxorubicin, vincristine a me kahi steroid i kapa ʻia he prednisolone.
CHOEP - like me CHOP akā me kahi chemotherapy hou i kapa ʻia ʻo etoposide.
- Ke komo ʻana i ka hoʻokolohua lapaʻau
Lapaʻau no nā keiki me ALK +ve ALCL
Nui nā keiki me ka lymphoma e hāʻawi ʻia e komo i nā hoʻokolohua lapaʻau. ʻOi aku ka maikaʻi e kamaʻilio me ke kauka haematologist o kāu keiki e pili ana i nā koho lapaʻau maikaʻi loa no kāu keiki, no ka mea, ʻokoʻa paha lākou mai nā mea i helu ʻia ma aneʻi.
ʻO ALK -ve ALCL pūnaewele kahi ʻano lymphoma maʻamau a paʻakikī no laila pono ʻoe e hoʻomaka i ka lapaʻau ma hope koke o kou ʻike ʻia ʻana. ʻO ka lāʻau lapaʻau no ka ALK -ve ALCL pūnaewele ua like me ka ALK +ve ALCL pūnaewele a hiki ke hoʻokomo i ka chemotherapy me ka radiotherapy a i ʻole.
- ʻO Chemotherapy - ʻO nā protocols chemotherapy maʻamau i hoʻohana ʻia no ka ALCL systemic:
BvCHP - cyclophosphamide, doxorubicin, prednisolone a me kahi antibody monoclonal i kapa ʻia ʻo brentuximab vedotin (Bv). Hoʻohana wale ʻo Bv i nā lymphomas me kahi pūmua i kapa ʻia ʻo CD30 ma luna o lākou.
kua - ka chemotherapy hui pū o cyclophosphamide, doxorubicin, vincristine a me kahi steroid i kapa ʻia he prednisolone.
CHOEP - like me CHOP akā me kahi chemotherapy hou i kapa ʻia ʻo etoposide.
- Ka hoʻololi ʻana o ka pūnaʻi kumu – Hiki iā ʻoe ke hāʻawi ʻia i ka chemotherapy kiʻekiʻe a ukali ʻia e kahi transplant cell stem inā loaʻa iā ʻoe ka systemic ALK-ve ALCL. E aʻo hou aʻe e pili ana i ka hoʻololi ʻana i ka stem cell ma ke kaomi ʻana ma aneʻi.
- Ke komo ʻana i ka hoʻokolohua lapaʻau
Nā ho'āʻo hoʻokolohua
Manaʻo ʻia ʻo kēlā me kēia manawa e pono ai ʻoe e hoʻomaka i nā lāʻau lapaʻau hou, e nīnau ʻoe i kāu kauka e pili ana i nā hoʻokolohua lapaʻau āu e ʻae ai. He mea nui nā hoʻokolohua lapaʻau no ka loaʻa ʻana o nā lāʻau hou, a i ʻole nā hui pū ʻana o nā lāʻau e hoʻomaikaʻi ai i ka mālama ʻana i ka ALCL i ka wā e hiki mai ana.
Hiki iā lākou ke hāʻawi iā ʻoe i kahi manawa e hoʻāʻo ai i kahi lāʻau hou, hui pū ʻana o nā lāʻau lapaʻau a i ʻole nā lāʻau lapaʻau ʻē aʻe āu e hiki ʻole ke loaʻa ma waho o ka hoʻokolokolo.
Nui nā lāʻau lapaʻau a me nā hui hoʻoponopono hou e hoʻāʻo ʻia nei i nā hoʻokolohua lapaʻau a puni ka honua no nā poʻe maʻi me ka maʻi ALC hou a hoʻi hou.L.
Nā hopena maʻamau o ka lāʻau lapaʻau
ʻO nā hopena ʻaoʻao o ka lāʻau lapaʻau e pili ana i ke ʻano o ka mālama ʻana iā ʻoe, ka wahi a me ka nui o kāu lymphoma a me nā kumu ʻē aʻe. He mea nui e hoʻomaopopo i ka mea maʻamau, a me nā hopena koʻikoʻi loa o kāu mālama ʻana. E kamaʻilio me kāu kauka a kahu kahu maʻi maʻi kūikawā paha e pili ana i nā hopena ʻaoʻao i manaʻo ʻia o kāu lapaʻau.
ʻO kekahi mau nīnau āu e noʻonoʻo ai e noʻonoʻo iā lākou:
- He aha ka inoa o ka lāʻau lapaʻau aʻu e loaʻa nei?
- He aha ke ʻano o ka lapaʻau ʻana (he chemotherapy, a i ʻole he antibody monoclonal etc.)?
- He aha nā hopena ʻaoʻao maʻamau a hiki i ka lāʻau lapaʻau?
- He aha nā hopena ʻaoʻao āu e pono ai e hōʻike i ka hui lapaʻau?
- He aha nā helu hoʻopili, a ma hea e hele ai inā pilikia 7 lā o ka pule a me 24 mau hola i kēlā me kēia lā?
No ka ʻike maʻamau e pili ana i nā hopena ʻaoʻao maʻamau a pehea e mālama ai iā lākou, e kaomi i ka loulou ma lalo nei.
ALCL hoʻihoʻi hou a i ʻole refractory
Ma hope o ka mālama ʻana, hiki i nā mea maʻi ke loaʻa i kahi manawa o kala kala (ʻaʻohe hōʻailona o ka lymphoma a i ʻole ke mālama ʻia ka lymphoma). I kekahi mau maʻi e hoʻi hou mai ka lymphoma (kau hou) a i ʻole i nā hihia koʻikoʻi ʻaʻole i pane i ka lāʻau lapaʻau mua (hale hōʻoluʻolu).Inā loaʻa kēia, aia kekahi mau lāʻau lapaʻau ʻē aʻe i hiki ke holomua a hiki ke komo:
- ʻO Pralatrexate
- Romidepsin
- ʻO Vorinostat (no ka PcALCL i hoʻihoʻi ʻia a i ʻole ka refractory)
- Brentuximab vedotin (Adcetris)
- ʻO ka chemotherapy hui
- Hoʻoponoponoʻia ka hopena
- Ke kuʻi ʻōnaʻi ʻōnaeho
Nā ho'āʻo hoʻokolohua
Manaʻo ʻia ʻo kēlā me kēia manawa e pono ai ʻoe e hoʻomaka i nā lāʻau lapaʻau hou, e nīnau ʻoe i kāu kauka e pili ana i nā hoʻokolohua lapaʻau āu e ʻae ai. He mea nui nā hoʻokolohua lapaʻau no ka loaʻa ʻana o nā lāʻau hou, a i ʻole nā hui pū ʻana o nā lāʻau e hoʻomaikaʻi ai i ka mālama ʻana i ka ALCL i ka wā e hiki mai ana.
Hiki iā lākou ke hāʻawi iā ʻoe i kahi manawa e hoʻāʻo ai i kahi lāʻau hou, hui pū ʻana o nā lāʻau lapaʻau a i ʻole nā lāʻau lapaʻau ʻē aʻe āu e hiki ʻole ke loaʻa ma waho o ka hoʻokolokolo.
Nui nā lāʻau lapaʻau a me nā hui hoʻoponopono hou e hoʻāʻo ʻia nei i nā hoʻokolohua lapaʻau a puni ka honua no nā poʻe maʻi me ka maʻi ALC hou a hoʻi hou.L.
He aha kāu e manaʻo ai ke pau ka mālama ʻana
Ke hoʻopau ʻoe i kāu mālama ʻana, makemake mau kāu kauka hematologist e ʻike mau iā ʻoe. E loaʻa iā ʻoe nā mākaʻikaʻi maʻamau me nā hoʻāʻo koko a me nā scans. ʻEhia ka manawa e loaʻa ai kēia mau hoʻāʻo ʻana ma muli o kou kūlana ponoʻī, a hiki i kāu kauka haematologist ke haʻi iā ʻoe i ka nui o ko lākou makemake e ʻike iā ʻoe.
He manawa hoʻohauʻoli a pilikia paha ke hoʻopau ʻoe i ka mālama ʻana - i kekahi manawa ʻelua. ʻAʻohe ala kūpono a hewa ʻole. Akā, he mea nui e kamaʻilio e pili ana i kou mau manaʻo a me kāu mea e pono ai me kāu poʻe aloha.
Loaʻa ke kākoʻo inā pilikia ʻoe i ka hoʻopau ʻana i ka lāʻau lapaʻau. E kamaʻilio me kāu hui lapaʻau - kāu kauka haematologist a i ʻole kahu maʻi maʻi maʻi kūikawā no ka mea hiki iā lākou ke kuhikuhi iā ʻoe no nā lawelawe aʻoaʻo i loko o ka haukapila. Hiki i kāu kauka kūloko (ke kauka lapaʻau - GP) ke kōkua pū me kēia.
Nā kahu hānai Lymphoma
Hiki iā ʻoe ke kamaʻilio pū me kā mākou Lymphoma Care Nurses. E kaomi wale i ka pihi "Contact Us" ma lalo o ka pale no nā kikoʻī pili.
Nā hopena hope
I kekahi manawa hiki ke hoʻomau ʻia ka hopena ʻaoʻao mai ka mālama ʻana, a i ʻole e ulu aʻe nā mahina a i ʻole mau makahiki ma hope o kou hoʻopau ʻana i ka mālama ʻana. Kapa ʻia kēia a hope-hopena. He mea nui e hōʻike i nā hopena hope loa i kāu hui lapaʻau i hiki iā lākou ke loiloi iā ʻoe a aʻo iā ʻoe pehea e hoʻokele maikaʻi ai i kēia mau hopena. Hiki i kekahi mau hopena hope ke komo:
- Hoʻololi i kou puʻuwai puʻuwai a i ʻole ke kūkulu ʻana
- Nā hopena i kou māmā
- ʻO ke kino neuropathy
- Hiki i nā hoʻololi Hormonal
- Hoʻololi ke ʻano.
Inā ʻike ʻoe i kekahi o kēia mau hopena hope loa, hiki i kāu haematologist a i ʻole kauka lapaʻau ke ʻōlelo aku iā ʻoe e ʻike i kekahi loea e hoʻokele i kēia mau hopena a hoʻomaikaʻi i kou ola maikaʻi. He mea nui naʻe e hōʻike i nā hopena hou a i ʻole nā hopena mau loa i ka hikiwawe no nā hopena maikaʻi loa.
Ola - Noho me a ma hope o ka maʻi kanesa
ʻO ke ola olakino, a i ʻole kekahi mau loli ola maikaʻi ma hope o ka mālama ʻana he mea kōkua nui ia i kou ola hou ʻana. Nui nā mea hiki iā ʻoe ke hana e kōkua iā ʻoe e noho maikaʻi me ALCL.
He nui ka poʻe i ʻike ma hope o ka hōʻoia ʻana i ka maʻi maʻi a i ʻole ka mālama ʻana, e loli ana kā lākou mau pahuhopu a me nā mea nui i ke ola. ʻO ka ʻike ʻana i ke ʻano o kāu 'maʻamau hou' hiki ke hoʻolōʻihi i ka manawa a hoʻonāukiuki. He ʻokoʻa paha nā manaʻolana o kou ʻohana a me kou mau hoaaloha. Hiki paha iā ʻoe ke kaʻawale, luhi a i ʻole kekahi mau manaʻo like ʻole e loli i kēlā me kēia lā.
ʻO nā pahuhopu nui ma hope o ka mālama ʻana i kāu ALCL ʻo ka hoʻi ʻana i ke ola a:
- e ʻeleu i kāu hana, ʻohana, a me nā kuleana ola ʻē aʻe
- e hoʻemi i nā hopena ʻaoʻao a me nā hōʻailona o ka maʻi kanesa a me ka mālama ʻana
- ʻike a mālama i nā hopena hope loa
- kōkua iā ʻoe e kūʻokoʻa e like me ka hiki
- hoʻomaikaʻi i kou maikaʻi o ke ola a mālama i ke olakino noʻonoʻo maikaʻi.
Hiki ke hāʻawi ʻia iā ʻoe nā ʻano hoʻolaʻa maʻi kanesa. Hiki i kēia ke manaʻo i kekahi o ka laulā ākea o na lawelawe e like me:
- kino kino, hooponopono eha
- hoʻolālā meaʻai a me ka hoʻoikaika kino
- ka manaʻo, ka ʻoihana a me ke aʻo kālā.
Hiki ke kōkua pū i ke kamaʻilio ʻana me kāu kauka kūloko e pili ana i nā papahana olakino kūloko e loaʻa ana no ka poʻe e hoʻōla ana mai kahi maʻi maʻi maʻi. Nui nā wahi kūloko e holo i ka hoʻoikaika kino a i ʻole nā hui kaiaulu a i ʻole nā papahana olakino ʻē aʻe e kōkua iā ʻoe e hoʻi i kāu hoʻomaʻamaʻa mua.
hōʻuluʻulu manaʻo
- ʻO Anaplastic Large Cell Lymphoma (ALCL) kahi ʻano o Non-Hodgkin Lymphoma a me kahi subtype o Peripheral T-cell Lymphoma (PTCL).
- Hoʻomaka ia i ka hoʻololi ʻana o kāu lymphocytes T-cell a lilo i ka maʻi kanesa.
- Hana ʻia nā pūnae T i loko o ko mākou iwi iwi akā hele i, a oʻo i loko o ko mākou thymus. Hiki iā lākou ke hele i kēlā me kēia wahi o ko mākou kino e hakakā i ka maʻi a me ka maʻi.
- ʻEhā mau ʻano ʻano like ʻole o ALCL a hiki iā lākou ke molowa a i ʻole ka huhū.
- ʻO ka mālama ʻana no ka ALCL e hilinaʻi ʻia ma ke ʻano subtype a me ka pae o ka ALCL i loaʻa iā ʻoe, a inā he molowa a i ʻole ka huhū.
- Hiki i ka ALCL ke pane maikaʻi i ka lāʻau lapaʻau a hiki iā ʻoe ke hele i kahi manawa kala ʻia akā naʻe, ʻaʻole maʻamau ka hoʻi hou ʻana no laila pono ʻoe e lapaʻau ʻoi aku ma mua o hoʻokahi manawa.
- E hōʻike i nā mea hou a i ʻole nā ʻino nā hōʻailona i kāu kauka pū kekahi B-hōʻailona.
- ʻAʻole ʻoe hoʻokahi. E kelepona aku i kāu hui hematology a i ʻole GP inā pono ʻoe, a i ʻole e kelepona i kā mākou Lymphoma Care Nurses ma ke kaomi ʻana i ke pihi "Contact Us" ma lalo o ka pale.