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Pamusoro peLymphoma

Kurapa kwe lymphoma

Nhanho ye lymphoma inotarisa kuti yakawanda sei yemuviri wako inobatwa ne lymphoma, uye inopa ruzivo rwemhando dzakanakisisa dzekurapa kwauri dzichava.

Pane iri peji:

Chii chinonzi staging?

Staging inoreva kuwanda kwemuviri wako kukanganiswa ne lymphoma yako - kana kuti yakapararira zvakadii kubva payakatanga.

Lymphocytes inogona kufamba kune chero chikamu chemuviri wako. Izvi zvinoreva kuti masero e-lymphoma (kenza lymphocytes), anogonawo kuenda kune chero chikamu chemuviri wako. Iwe unozofanirwa kuita bvunzo dzakawanda kuti uwane ruzivo urwu. Bvunzo idzi dzinonzi staging tests uye kana wawana zvabuda, unoona kuti une danho rekutanga (I), danho repiri (II), danho rechitatu (III) kana danho rechina (IV) lymphoma.

Staging Lymphoma - Iyo Ann Arbor kana Lugano Staging System

Nhanho yako ye lymphoma ichaenderana ne:

  • Ingani nzvimbo dzemuviri wako dzine lymphoma
  • Apo lymphoma inosanganisira kana iri pamusoro, pasi kana kumativi ose maviri e diaphragm yako (musuru mukuru, wakaita dome pasi pembabvu yako inoparadzanisa chipfuva chako kubva mudumbu rako)
  • Kunyangwe iyo lymphoma yakapararira kumapfupa ako emapfupa kana dzimwe nhengo dzakadai sechiropa chako, mapapu, ganda kana pfupa.

Matanho I uye II anonzi 'kutanga kana nhanho diki' (inosanganisira nzvimbo shoma yemuviri wako).

Matanho III neIV anonzi 'advanced stage' (yakawanda). Zvakakosha kuziva kuti kusiyana nemamwe magomarara, mazhinji epamberi aggressive lymphoma anogona kurapwa. Taura nachiremba nezvemikana yako yekurapwa kana kuregererwa kwenguva refu.

Kurapa kwe lymphoma
Danho 1 uye 2 lymphoma inoonekwa sekutanga, uye nhanho 3 ne 4 inonzi advanced stage lymphoma.
Stage 1

Imwe lymph node area inobatwa, kungave pamusoro kana pasi pe diaphragm*.

Stage 2

Nzvimbo mbiri kana kupfuura dze lymph node dzinobatwa kune rimwe divi re diaphragm *.

Stage 3

Inenge imwe lymph node nzvimbo kumusoro uye imwe lymph node nzvimbo iri pasi pe diaphragm* inobatwa.

Stage 4

Lymphoma iri mumalymph nodes akawanda uye yapararira kune dzimwe nhengo dzemuviri (semumapfupa, mapapu, chiropa).

Diaphragm
Diaphragm yedu imhasuru yakaita dome inomhanya nepasi pemapapu edu uye inoparadzanisa chipfuva chedu nedumbu redu. Zvinobatsirawo kutamisa mapapu edu kumusoro nekudzika patinofema.

Kuwedzera ruzivo rwekuita

Chiremba wako anogonawo kutaura nezvedanho rako achishandisa tsamba, senge A, B, E, X kana S. Mavara aya anopa mamwe mashoko pamusoro pezviratidzo zvaunazvo kana kuti muviri wako uri kukanganiswa sei ne lymphoma. Ruzivo rwese urwu runobatsira chiremba wako kuwana chirongwa chekurapa chakanakira iwe. 

tsamba
zvichireva
kukosha

A kana B

  • A = hauna B-zviratidzo
  • B = une B-zviratidzo
  • Kana uine B zviratidzo paunoonekwa, unogona kunge uine chirwere chepamusoro-soro.
  • Unogona kunge uchiri kurapwa kana kupinda mukuregererwa, asi unozoda kurapwa kwakanyanya

E & X

  • E = une danho rekutanga (I kana II) lymphoma ine nhengo iri kunze kwe lymph system - Izvi zvinogona kusanganisira chiropa chako, mapapu, ganda, dundira kana chero imwe nhengo 
  • X = une bundu guru rinodarika 10cm mukukura. Izvi zvinonziwo "bulky disease"
  • Kana iwe wakamboonekwa kuti une nhanho shoma ye lymphoma, asi iri mune imwe yenhengo dzako kana inoonekwa seyakakura, chiremba wako anogona kushandura nhanho yako kusvika padanho repamusoro.
  • Unogona kunge uchiri kurapwa kana kupinda mukuregererwa, asi unozoda kurapwa kwakanyanya

S

  • S = une lymphoma mune spleen yako
  • Ungada kuvhiyiwa kubvisa spleen yako

(Spleen yedu inhengo iri mukati medu lymphatic hurongwa iyo inosefa nekuchenesa ropa redu, uye inzvimbo yedu B-masero anozorora uye kugadzira masoja ekudzivirira chirwere)

Miedzo yekutamba

Kuti uzive kuti ndeipi nhanho yauinayo, unogona kukumbirwa kuti uite mamwe eanotevera nhanho bvunzo:

Computed tomography (CT) scan

Aya ma scans anotora mifananidzo yemukati mechipfuva chako, dumbu kana pelvis. Vanopa mifananidzo yakadzama inopa ruzivo rwakawanda kupfuura yakajairwa X-ray.

Positron emission tomography (PET) scan 

Iyi scan inotora mifananidzo yemukati memuviri wako wese. Iwe uchapihwa uye tsono nemumwe mushonga masero ane kenza - senge lymphoma masero anotora. Mushonga unobatsira PET scan kuona kuti lymphoma iripi uye saizi uye chimiro nekusimbisa nzvimbo dzine lymphoma masero. Nzvimbo idzi dzimwe nguva dzinonzi "zvinopisa".

Lumbar kubaya

Central nervous system inosanganisira uropi hwako uye musana. Aya akakomberedzwa nemvura inonzi cerebral spinal fluidA lumbar puncture inzira yakaitwa yekutarisa kana uine chero lymphoma mune yako yepakati tsinga system (CNS), iyo inosanganisira uropi hwako, musana uye nzvimbo yakapoteredza maziso ako. Iwe unozofanirwa kugara wakanyarara panguva yekuitwa, kuitira kuti vacheche nevana vanogona kupihwa mushonga wekuti varare kwechinguva chidiki kana chirongwa ichi chaitwa. Vazhinji vanhu vakuru vanongoda mushonga wekutindivadza wepanzvimbo kuitira kuti maitiro aite chiveve nzvimbo.

Chiremba wako achaisa tsono kumusana kwako, uye oburitsa mvura shoma inonzi “cerebral spinal fluid” (CSF) kubva pakatenderedza musana wako. CSF imvura inoita zvishoma sechinhu chinokatyamadza kuCNS yako. Inotakurawo mapuroteni akasiyana uye hutachiona hunorwisa masero edziviriro senge lymphocytes kuchengetedza uropi hwako uye musana. CSF inogonawo kubatsira kubvisa chero mvura yakawedzerwa yaungave uine muuropi hwako kana kutenderedza musana wako kudzivirira kuzvimba munzvimbo idzodzo.

Sampuli yeCSF inozotumirwa kune pathology uye kuongororwa chero zviratidzo zve lymphoma.

Bone marora bhiopsy
A bone marrow biopsy inoitwa kuti uone kana pane lymphoma muropa rako kana bone marrow. Mwongo wako ndicho chipanje, chikamu chepakati chemapfupa ako panogadzirwa masero ako eropa. Pane masampuli maviri chiremba achatora kubva munzvimbo ino anosanganisira:
 
  • Bone marrow aspirate (BMA): bvunzo iyi inotora shoma shoma yemvura inowanikwa munzvimbo yemwongo.
  • Bone marrow aspirate trephine (BMAT): bvunzo iyi inotora diki diki yemwongo tishu.
bone marrow biopsy kuongorora kana nhanho lymphoma
A bone marrow biopsy inogona kuitwa kubatsira kuongorora kana danho lymphoma

Iwo masampuli anobva atumirwa kune pathology uko anotariswa zviratidzo zve lymphoma.

Maitirwo emuwongo biopsies anogona kusiyana zvichienderana nekuti uri kurapwa kupi, asi kazhinji anozosanganisira mushonga wekutindivadza wepanzvimbo kuti uite chiveve nzvimbo.

Mune zvimwe zvipatara, unogona kupihwa light sedation iyo inokubatsira kuti uzorore uye inogona kukumisa kuyeuka maitiro. Zvisinei vanhu vazhinji havadi izvi uye vanogona kunge vaine "muridzo yegirinhi" yekuyamwa. Iyi muridzo yegirinhi ine mushonga wekuuraya marwadzo mairi (unonzi Penthrox kana methoxyflurane), waunoshandisa sezvinodiwa mukati memaitiro ese.

Ita shuwa kuti unobvunza chiremba wako izvo zviripo kuti uwedzere kugadzikana panguva yekuita, uye taura navo pamusoro pezvaunofunga kuti ichava sarudzo yakanakira iwe.

Ruzivo rwakawanda pamusoro pemapfupa biopsies anogona kuwanikwa pane yedu peji rewebhu pano.

Kumira kweCLL - Iyo RAI staging system

Kuzvimba lymph node
Lymph nodes anozara nekenza B-masero anogona kuzvimba nebundu rinoonekwa.

Kuronga kweCLL kwakasiyana zvishoma kune mamwe ma subtypes e lymphoma, nokuti CLL inotanga muropa uye mwongo.

Iyo RAI staging system inotarisa kuCLL yako kuti uone kana iwe uchidaro, kana kuti hauna chimwe chezvinotevera:

  • yakakwirira ye lymphocytes muropa rako kana mwongo - iyi inonzi lymphocytosis (lim-foe-cy-toe-sis)
  • kuzvimba lymph nodes - lymphadenopathy (limf-a-den-op-ah-thee)
  • spleen yakakura - splenomegaly (splen-oh-meg-ah-lee)
  • kuderera kwemasero matsvuku eropa muropa rako - anemia (a-nee-mee-yah)
  • kuderera kwemaplatelet muropa rako - thrombocytopenia (throm-bow-cy-toe-pee-nee-yah)
  • chiropa chakawedzera - hepatomegaly (hep-at-o-meg-a-lee)

 

Zvinorehwa nhanho imwe neimwe yeRAI

 
RAI chikamu 0Lymphocytosis uye pasina kuwedzera kwemalymph nodes, spleen, kana chiropa, uye nechepedyo sero tsvuku yeropa uye platelet kuverenga.
RAI chikamu 1Lymphocytosis uye lymph nodes yakakura. Spleen nechiropa hazvina kukura uye sero dzvuku reropa uye maplatelet kuverenga zvakajairika kana zvishoma zvishoma.
RAI chikamu 2Lymphocytosis pamwe nespleen yakakura (uye pamwe chiropa chakawedzera), ine kana isina lymph nodes yakakura. Sero dzvuku reropa uye nhamba dzeplatelet zvakajairika kana kuti zvishoma zvishoma
RAI chikamu 3Lymphocytosis pamwe neanemia (masero matsvuku eropa mashoma), ane kana asina ma lymph nodes akawedzera, spleen, kana chiropa. Nhamba dzeplatelet dzave pedyo neakajairika.
RAI chikamu 4Lymphocytosis plus thrombocytopenia (maplatelet mashoma), ane kana asina anemia, lymph nodes yakakura, spleen, kana chiropa.

*Lymphocytosis zvinoreva ma lymphocyte akawandisa muropa rako kana mwongo

Clinical Grading yeLymphoma

Masero ako e-lymphoma ane maitiro akasiyana ekukura, uye anotaridzika akasiyana kune akajairwa maseru. Giredhi ye lymphoma yako inokurumidza kukurumidza masero ako lymphoma kukura, iyo inokanganisa nzira yekutarisa pasi pe microscope. Iwo mamakisi ari Magiredhi 1-4 (akaderera, epakati, akakwirira). Kana uine giredhi repamusoro lymphoma, masero ako e-lymphoma anotaridzika zvakanyanya kusiyana nemasero akajairwa, nekuti ari kukura nekukurumidza kuti akure zvakanaka. Mhedziso yemagiredhi iri pazasi.

  • G1 - giredhi yakaderera - masero ako anotaridzika padyo neakajairika, uye anokura uye anopararira zvishoma nezvishoma.  
  • G2 - giredhi repakati - maseru ako ari kutanga kutaridzika zvakasiyana asi mamwe maseru akajairwa aripo, uye anokura nekupararira pamwero wepakati.
  • G3 - giredhi repamusoro - maseru ako anotaridzika zvakasiyana nemaseru mashoma akajairwa, uye anokura nekupararira nekukurumidza. 
  • G4 - giredhi repamusoro - maseru ako anotaridzika zvakasiyana kune akajairwa, uye anokura nekupararira nekukurumidza.

Ruzivo rwese urwu runowedzera kumufananidzo wose unovaka chiremba wako kuti akubatsire kusarudza mhando yekurapa yakanakira iwe. 

Zvakakosha kuti utaure nachiremba wako nezve njodzi yako pachako kuitira kuti uve neruzivo rwakajeka rwezvaunotarisira kubva mukurapwa kwako.

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